Appears as meningocele crossed by fibroneurovascular stable that extends from dorsal aspect of spinal cord to attach to dome of meningocele sac
Complete form
Hydromyelic cavity within sac is continuous with ependymal canal of spinal cord
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Muthukumar N: Terminal myelocystocele with holocord syringomyelia: short report. J Pediatr Neurosci. 8(2):171-2, 2013
Barkovich AJ et al: Pediatric Neuroimaging. Fifth edition. Philadelphia, PA: Lippincott Williams & Wilkins. 888-90, 2012
Pang D et al: Terminal myelocystocele: surgical observations and theory of embryogenesis. Neurosurgery. 70(6):1383-404; discussion 1404-5, 2012
Tandon V et al: Terminal myelocystocele: a series of 30 cases and review of the literature. Pediatr Neurosurg. 48(4):229-35, 2012
Hashiguchi K et al: Holocord hydrosyringomyelia with terminal myelocystocele revealed by constructive interference in steady-state MR imaging. Pediatr Neurosurg. 44(6):509-12, 2008
Morioka T et al: Neurosurgical management of occult spinal dysraphism associated with OEIS complex. Childs Nerv Syst. 24(6):723-9, 2008
Rossi A et al: Spectrum of nonterminal myelocystoceles. Neurosurgery. 58(3):509-15; discussion 509-15, 2006
Gupta DK et al: Terminal myelocystoceles: a series of 17 cases. J Neurosurg. 103(4 Suppl):344-52, 2005
Tortori-Donati P et al: Pediatric Neuroradiology. Heidelburg, Germany. 1574-1576, 2005
Rossi A et al: Imaging in spine and spinal cord malformations. Eur J Radiol. 50(2):177-200, 2004
Tortori-Donati P et al: Spinal dysraphism: a review of neuroradiological features with embryological correlations and proposal for a new classification. Neuroradiology. 42(7):471-91, 2000
Byrd SE et al: Imaging of terminal myelocystoceles. J Natl Med Assoc. 88(8):510-6, 1996
Steinbok P et al: Cervical meningoceles and myelocystoceles: a unifying hypothesis. Pediatr Neurosurg. 23(6):317-22, 1995
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Syringocele, lipomyelocystocele
Definitions
Closed spinal dysraphism characterized by syrinx associated with neural placode protruding outside of spinal canal through osseous dysraphic defect
Terminal and nonterminal subtypes
Terminal myelocystocele is spinal dysraphism involving caudal-most aspect of spinal cord
Appears as meningocele crossed by fibroneurovascular stable that extends from dorsal aspect of spinal cord to attach to dome of meningocele sac
Complete form
Hydromyelic cavity within sac is continuous with ependymal canal of spinal cord
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Muthukumar N: Terminal myelocystocele with holocord syringomyelia: short report. J Pediatr Neurosci. 8(2):171-2, 2013
Barkovich AJ et al: Pediatric Neuroimaging. Fifth edition. Philadelphia, PA: Lippincott Williams & Wilkins. 888-90, 2012
Pang D et al: Terminal myelocystocele: surgical observations and theory of embryogenesis. Neurosurgery. 70(6):1383-404; discussion 1404-5, 2012
Tandon V et al: Terminal myelocystocele: a series of 30 cases and review of the literature. Pediatr Neurosurg. 48(4):229-35, 2012
Hashiguchi K et al: Holocord hydrosyringomyelia with terminal myelocystocele revealed by constructive interference in steady-state MR imaging. Pediatr Neurosurg. 44(6):509-12, 2008
Morioka T et al: Neurosurgical management of occult spinal dysraphism associated with OEIS complex. Childs Nerv Syst. 24(6):723-9, 2008
Rossi A et al: Spectrum of nonterminal myelocystoceles. Neurosurgery. 58(3):509-15; discussion 509-15, 2006
Gupta DK et al: Terminal myelocystoceles: a series of 17 cases. J Neurosurg. 103(4 Suppl):344-52, 2005
Tortori-Donati P et al: Pediatric Neuroradiology. Heidelburg, Germany. 1574-1576, 2005
Rossi A et al: Imaging in spine and spinal cord malformations. Eur J Radiol. 50(2):177-200, 2004
Tortori-Donati P et al: Spinal dysraphism: a review of neuroradiological features with embryological correlations and proposal for a new classification. Neuroradiology. 42(7):471-91, 2000
Byrd SE et al: Imaging of terminal myelocystoceles. J Natl Med Assoc. 88(8):510-6, 1996
Steinbok P et al: Cervical meningoceles and myelocystoceles: a unifying hypothesis. Pediatr Neurosurg. 23(6):317-22, 1995
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