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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Enteric cyst, enterogenous cyst, endodermal cyst
Definitions
- Cyst along neuraxis lined with mucin-secreting cuboidal or columnar epithelium resembling alimentary tract
- Derived from displaced endodermal tissue
- Classified within split notochord syndrome spectrum of complex closed spinal dysraphism without subcutaneous mass
- Neurenteric cyst is on mild end of spectrum
- Dorsal enteric fistula is on severe end
- Intestinal cavity communicates with dorsal skin surface in midline, traversing prevertebral soft tissues, vertebral bodies, spinal canal, & posterior elements
- Cyst along neuraxis lined with mucin-secreting cuboidal or columnar epithelium resembling alimentary tract
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Anderson T et al: Intracranial neurenteric cyst: a case report and differential diagnosis of intracranial cystic lesions. Radiol Case Rep. 15(12):2649-54, 2020
- Barkovich AJ et al: Pediatric Neuroimaging. 6th ed. Wolters Kluwer. 681-3, 2019
- Shimizu Y et al: A rare presentation of a pediatric neurenteric cyst as an intra-axial pontine lesion: a case report with a 5-year follow-up. Surg Neurol Int. 10:236, 2019
- Viaene AN et al: Recurrent neurenteric cysts compressing the brainstem. Surg Neurol Int. 10:245, 2019
- Kitamura Y et al: Supratentorial neurenteric cyst with spontaneous repetitive intracystic hemorrhage mimicking brain abscess: a case report. Neurosurg Rev. 37(1):153-9, 2014
- Al-Ahmed IH et al: Neurosurgical management of neurenteric cysts in children. J Neurosurg Pediatr. 11(5):511-7, 2013
- Gauden AJ et al: Intracranial neuroenteric cysts: a concise review including an illustrative patient. J Clin Neurosci. 19(3):352-9, 2012
- Jhawar SS et al: Intramedullary spinal neurenteric cyst with fluid-fluid level. J Neurosurg Pediatr. 9(5):542-5, 2012
- Savage JJ et al: Neurenteric cysts of the spine. J Craniovertebr Junction Spine. 1(1):58-63, 2010
- Theret E et al: Huge intramedullar neurenteric cyst with intrathoracic development in a 1 month-old boy: excision though the anterior approach. A case report and review of the literature. Acta Neurochir (Wien). 152(3):481-3, 2010
- Aydin AL et al: Prenatal diagnosis of a large, cervical, intraspinal, neurenteric cyst and postnatal outcome. J Pediatr Surg. 44(9):1835-8, 2009
- Surash S et al: Malignant transformation of a neurenteric cyst in the posterior fossa following complete excision. Br J Neurosurg. 23(4):458-61, 2009
- Asagiri K et al: A case of split notochord syndrome with congenital ileal atresia, the total absence of a colon, and a dorsal enteric cyst communicating to the retroperitoneal isolated ceca with a vesical fistula. Pediatr Surg Int. 24(9):1073-7, 2008
- Kimya Y et al: Prenatal diagnosis of the rarely observed split notochord syndrome. Ultrasound Obstet Gynecol. 29(6):712-3, 2007
- Preece MT et al: Intracranial neurenteric cysts: imaging and pathology spectrum. AJNR Am J Neuroradiol. 27(6):1211-6, 2006
- Tortori-Donati P et al: Pediatric Neuroradiology. Springer-Verla. 587, 2005
- Wakisaka M et al: Giant transdiaphragmatic duodenal duplication with an intraspinal neurenteric cyst as part of the split notochord syndrome: report of a case. Surg Today. 34(5):459-62, 2004
- Kapoor V et al: Neuroradiologic-pathologic correlation in a neurenteric cyst of the clivus. AJNR Am J Neuroradiol. 23(3):476-9, 2002
- Kumar R et al: Intraspinal neurenteric cysts--report of three paediatric cases. Childs Nerv Syst. 17(10):584-8, 2001
- Paleologos TS et al: Spinal neurenteric cysts without associated malformations. Are they the same as those presenting in spinal dysraphism? Br J Neurosurg. 14(3):185-94, 2000
- Brooks BS et al: Neuroimaging features of neurenteric cysts: analysis of nine cases and review of the literature. AJNR Am J Neuroradiol. 14(3):735-46, 1993
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Enteric cyst, enterogenous cyst, endodermal cyst
Definitions
- Cyst along neuraxis lined with mucin-secreting cuboidal or columnar epithelium resembling alimentary tract
- Derived from displaced endodermal tissue
- Classified within split notochord syndrome spectrum of complex closed spinal dysraphism without subcutaneous mass
- Neurenteric cyst is on mild end of spectrum
- Dorsal enteric fistula is on severe end
- Intestinal cavity communicates with dorsal skin surface in midline, traversing prevertebral soft tissues, vertebral bodies, spinal canal, & posterior elements
- Cyst along neuraxis lined with mucin-secreting cuboidal or columnar epithelium resembling alimentary tract
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Anderson T et al: Intracranial neurenteric cyst: a case report and differential diagnosis of intracranial cystic lesions. Radiol Case Rep. 15(12):2649-54, 2020
- Barkovich AJ et al: Pediatric Neuroimaging. 6th ed. Wolters Kluwer. 681-3, 2019
- Shimizu Y et al: A rare presentation of a pediatric neurenteric cyst as an intra-axial pontine lesion: a case report with a 5-year follow-up. Surg Neurol Int. 10:236, 2019
- Viaene AN et al: Recurrent neurenteric cysts compressing the brainstem. Surg Neurol Int. 10:245, 2019
- Kitamura Y et al: Supratentorial neurenteric cyst with spontaneous repetitive intracystic hemorrhage mimicking brain abscess: a case report. Neurosurg Rev. 37(1):153-9, 2014
- Al-Ahmed IH et al: Neurosurgical management of neurenteric cysts in children. J Neurosurg Pediatr. 11(5):511-7, 2013
- Gauden AJ et al: Intracranial neuroenteric cysts: a concise review including an illustrative patient. J Clin Neurosci. 19(3):352-9, 2012
- Jhawar SS et al: Intramedullary spinal neurenteric cyst with fluid-fluid level. J Neurosurg Pediatr. 9(5):542-5, 2012
- Savage JJ et al: Neurenteric cysts of the spine. J Craniovertebr Junction Spine. 1(1):58-63, 2010
- Theret E et al: Huge intramedullar neurenteric cyst with intrathoracic development in a 1 month-old boy: excision though the anterior approach. A case report and review of the literature. Acta Neurochir (Wien). 152(3):481-3, 2010
- Aydin AL et al: Prenatal diagnosis of a large, cervical, intraspinal, neurenteric cyst and postnatal outcome. J Pediatr Surg. 44(9):1835-8, 2009
- Surash S et al: Malignant transformation of a neurenteric cyst in the posterior fossa following complete excision. Br J Neurosurg. 23(4):458-61, 2009
- Asagiri K et al: A case of split notochord syndrome with congenital ileal atresia, the total absence of a colon, and a dorsal enteric cyst communicating to the retroperitoneal isolated ceca with a vesical fistula. Pediatr Surg Int. 24(9):1073-7, 2008
- Kimya Y et al: Prenatal diagnosis of the rarely observed split notochord syndrome. Ultrasound Obstet Gynecol. 29(6):712-3, 2007
- Preece MT et al: Intracranial neurenteric cysts: imaging and pathology spectrum. AJNR Am J Neuroradiol. 27(6):1211-6, 2006
- Tortori-Donati P et al: Pediatric Neuroradiology. Springer-Verla. 587, 2005
- Wakisaka M et al: Giant transdiaphragmatic duodenal duplication with an intraspinal neurenteric cyst as part of the split notochord syndrome: report of a case. Surg Today. 34(5):459-62, 2004
- Kapoor V et al: Neuroradiologic-pathologic correlation in a neurenteric cyst of the clivus. AJNR Am J Neuroradiol. 23(3):476-9, 2002
- Kumar R et al: Intraspinal neurenteric cysts--report of three paediatric cases. Childs Nerv Syst. 17(10):584-8, 2001
- Paleologos TS et al: Spinal neurenteric cysts without associated malformations. Are they the same as those presenting in spinal dysraphism? Br J Neurosurg. 14(3):185-94, 2000
- Brooks BS et al: Neuroimaging features of neurenteric cysts: analysis of nine cases and review of the literature. AJNR Am J Neuroradiol. 14(3):735-46, 1993
