Cyst along neuraxis lined with mucin-secreting cuboidal or columnar epithelium resembling alimentary tract
Derived from displaced endodermal tissue
Classified within split notochord syndrome spectrum of complex closed spinal dysraphism without subcutaneous mass
Neurenteric cyst is on mild end of spectrum
Dorsal enteric fistula is on severe end
Intestinal cavity communicates with dorsal skin surface in midline, traversing prevertebral soft tissues, vertebral bodies, spinal canal, & posterior elements
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Anderson T et al: Intracranial neurenteric cyst: a case report and differential diagnosis of intracranial cystic lesions. Radiol Case Rep. 15(12):2649-54, 2020
Barkovich AJ et al: Pediatric Neuroimaging. 6th ed. Wolters Kluwer. 681-3, 2019
Shimizu Y et al: A rare presentation of a pediatric neurenteric cyst as an intra-axial pontine lesion: a case report with a 5-year follow-up. Surg Neurol Int. 10:236, 2019
Viaene AN et al: Recurrent neurenteric cysts compressing the brainstem. Surg Neurol Int. 10:245, 2019
Kitamura Y et al: Supratentorial neurenteric cyst with spontaneous repetitive intracystic hemorrhage mimicking brain abscess: a case report. Neurosurg Rev. 37(1):153-9, 2014
Al-Ahmed IH et al: Neurosurgical management of neurenteric cysts in children. J Neurosurg Pediatr. 11(5):511-7, 2013
Gauden AJ et al: Intracranial neuroenteric cysts: a concise review including an illustrative patient. J Clin Neurosci. 19(3):352-9, 2012
Jhawar SS et al: Intramedullary spinal neurenteric cyst with fluid-fluid level. J Neurosurg Pediatr. 9(5):542-5, 2012
Savage JJ et al: Neurenteric cysts of the spine. J Craniovertebr Junction Spine. 1(1):58-63, 2010
Theret E et al: Huge intramedullar neurenteric cyst with intrathoracic development in a 1 month-old boy: excision though the anterior approach. A case report and review of the literature. Acta Neurochir (Wien). 152(3):481-3, 2010
Aydin AL et al: Prenatal diagnosis of a large, cervical, intraspinal, neurenteric cyst and postnatal outcome. J Pediatr Surg. 44(9):1835-8, 2009
Surash S et al: Malignant transformation of a neurenteric cyst in the posterior fossa following complete excision. Br J Neurosurg. 23(4):458-61, 2009
Asagiri K et al: A case of split notochord syndrome with congenital ileal atresia, the total absence of a colon, and a dorsal enteric cyst communicating to the retroperitoneal isolated ceca with a vesical fistula. Pediatr Surg Int. 24(9):1073-7, 2008
Kimya Y et al: Prenatal diagnosis of the rarely observed split notochord syndrome. Ultrasound Obstet Gynecol. 29(6):712-3, 2007
Preece MT et al: Intracranial neurenteric cysts: imaging and pathology spectrum. AJNR Am J Neuroradiol. 27(6):1211-6, 2006
Tortori-Donati P et al: Pediatric Neuroradiology. Springer-Verla. 587, 2005
Wakisaka M et al: Giant transdiaphragmatic duodenal duplication with an intraspinal neurenteric cyst as part of the split notochord syndrome: report of a case. Surg Today. 34(5):459-62, 2004
Kapoor V et al: Neuroradiologic-pathologic correlation in a neurenteric cyst of the clivus. AJNR Am J Neuroradiol. 23(3):476-9, 2002
Kumar R et al: Intraspinal neurenteric cysts--report of three paediatric cases. Childs Nerv Syst. 17(10):584-8, 2001
Paleologos TS et al: Spinal neurenteric cysts without associated malformations. Are they the same as those presenting in spinal dysraphism? Br J Neurosurg. 14(3):185-94, 2000
Brooks BS et al: Neuroimaging features of neurenteric cysts: analysis of nine cases and review of the literature. AJNR Am J Neuroradiol. 14(3):735-46, 1993
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
Enteric cyst, enterogenous cyst, endodermal cyst
Definitions
Cyst along neuraxis lined with mucin-secreting cuboidal or columnar epithelium resembling alimentary tract
Derived from displaced endodermal tissue
Classified within split notochord syndrome spectrum of complex closed spinal dysraphism without subcutaneous mass
Neurenteric cyst is on mild end of spectrum
Dorsal enteric fistula is on severe end
Intestinal cavity communicates with dorsal skin surface in midline, traversing prevertebral soft tissues, vertebral bodies, spinal canal, & posterior elements
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Ultrasonographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Anderson T et al: Intracranial neurenteric cyst: a case report and differential diagnosis of intracranial cystic lesions. Radiol Case Rep. 15(12):2649-54, 2020
Barkovich AJ et al: Pediatric Neuroimaging. 6th ed. Wolters Kluwer. 681-3, 2019
Shimizu Y et al: A rare presentation of a pediatric neurenteric cyst as an intra-axial pontine lesion: a case report with a 5-year follow-up. Surg Neurol Int. 10:236, 2019
Viaene AN et al: Recurrent neurenteric cysts compressing the brainstem. Surg Neurol Int. 10:245, 2019
Kitamura Y et al: Supratentorial neurenteric cyst with spontaneous repetitive intracystic hemorrhage mimicking brain abscess: a case report. Neurosurg Rev. 37(1):153-9, 2014
Al-Ahmed IH et al: Neurosurgical management of neurenteric cysts in children. J Neurosurg Pediatr. 11(5):511-7, 2013
Gauden AJ et al: Intracranial neuroenteric cysts: a concise review including an illustrative patient. J Clin Neurosci. 19(3):352-9, 2012
Jhawar SS et al: Intramedullary spinal neurenteric cyst with fluid-fluid level. J Neurosurg Pediatr. 9(5):542-5, 2012
Savage JJ et al: Neurenteric cysts of the spine. J Craniovertebr Junction Spine. 1(1):58-63, 2010
Theret E et al: Huge intramedullar neurenteric cyst with intrathoracic development in a 1 month-old boy: excision though the anterior approach. A case report and review of the literature. Acta Neurochir (Wien). 152(3):481-3, 2010
Aydin AL et al: Prenatal diagnosis of a large, cervical, intraspinal, neurenteric cyst and postnatal outcome. J Pediatr Surg. 44(9):1835-8, 2009
Surash S et al: Malignant transformation of a neurenteric cyst in the posterior fossa following complete excision. Br J Neurosurg. 23(4):458-61, 2009
Asagiri K et al: A case of split notochord syndrome with congenital ileal atresia, the total absence of a colon, and a dorsal enteric cyst communicating to the retroperitoneal isolated ceca with a vesical fistula. Pediatr Surg Int. 24(9):1073-7, 2008
Kimya Y et al: Prenatal diagnosis of the rarely observed split notochord syndrome. Ultrasound Obstet Gynecol. 29(6):712-3, 2007
Preece MT et al: Intracranial neurenteric cysts: imaging and pathology spectrum. AJNR Am J Neuroradiol. 27(6):1211-6, 2006
Tortori-Donati P et al: Pediatric Neuroradiology. Springer-Verla. 587, 2005
Wakisaka M et al: Giant transdiaphragmatic duodenal duplication with an intraspinal neurenteric cyst as part of the split notochord syndrome: report of a case. Surg Today. 34(5):459-62, 2004
Kapoor V et al: Neuroradiologic-pathologic correlation in a neurenteric cyst of the clivus. AJNR Am J Neuroradiol. 23(3):476-9, 2002
Kumar R et al: Intraspinal neurenteric cysts--report of three paediatric cases. Childs Nerv Syst. 17(10):584-8, 2001
Paleologos TS et al: Spinal neurenteric cysts without associated malformations. Are they the same as those presenting in spinal dysraphism? Br J Neurosurg. 14(3):185-94, 2000
Brooks BS et al: Neuroimaging features of neurenteric cysts: analysis of nine cases and review of the literature. AJNR Am J Neuroradiol. 14(3):735-46, 1993
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