Batchala PP et al: Imaging of tumor syndromes. Radiol Clin North Am. 59(3):471-500, 2021
Ren Y et al: New developments in neurofibromatosis type 2 and vestibular schwannoma. Neurooncol Adv. 3(1):vdaa153, 2021
Slattery WH: Neurofibromatosis type 2. Otolaryngol Clin North Am. 48(3):443-60, 2015
Maniakas A et al: Neurofibromatosis type 2 vestibular schwannoma treatment: a review of the literature, trends, and outcomes. Otol Neurotol. 35(5):889-94, 2014
Koontz NA et al: Schwannomatosis: the overlooked neurofibromatosis? AJR Am J Roentgenol. 200(6):W646-53, 2013
Sughrue ME et al: A prospective study of hearing preservation in untreated vestibular schwannomas. J Neurosurg. 114(2):381-5, 2011
Hsu PW et al: Outcomes of 75 patients over 12 years treated for acoustic neuromas with linear accelerator-based radiosurgery. J Clin Neurosci. 17(5):556-60, 2010
Kissil JL et al: What's new in neurofibromatosis? Proceedings from the 2009 NF Conference: new frontiers. Am J Med Genet A. 152A(2):269-83, 2010
Mautner VF et al: Bevacizumab induces regression of vestibular schwannomas in patients with neurofibromatosis type 2. Neuro Oncol. 12(1):14-8, 2010
Suryanarayanan R et al: Vestibular schwannoma: role of conservative management. J Laryngol Otol. 124(3):251-7, 2010
Fisher LM et al: Concordance of bilateral vestibular schwannoma growth and hearing changes in neurofibromatosis 2: neurofibromatosis 2 natural history consortium. Otol Neurotol. 30(6):835-41, 2009
Plotkin SR et al: Hearing improvement after bevacizumab in patients with neurofibromatosis type 2. N Engl J Med. 361(4):358-67, 2009
Moffat DA et al: Management strategies in neurofibromatosis type 2. Eur Arch Otorhinolaryngol. 260(1):12-8, 2003
Brackmann DE et al: Early proactive management of vestibular schwannomas in neurofibromatosis type 2. Neurosurgery. 49(2):274-80; discussion 280-3, 2001
Gillespie JE: Imaging in neurofibromatosis type 2: screening using magnetic resonance imaging. Ear Nose Throat J. 78(2):102-3, 106, 108-9, 1999
Kiroğlu MM et al: Bilateral acoustic neurofibromatosis with bilateral multicentric facial schwannomas. Eur Arch Otorhinolaryngol. 253(4-5):305-8, 1996
Akeson P et al: Radiological investigation of neurofibromatosis type 2. Neuroradiology. 36(2):107-10, 1994
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TERMINOLOGY
Abbreviations
Neurofibromatosis type 2 (NF2)
Synonyms
Central neurofibromatosis, bilateral acoustic neurofibromatosis, schwannomatosis
Schwannomatosis now considered distinct form of neurofibromatosis, separate from NF1 & NF2
Largely diagnosed in adulthood as peripheral schwannomas with pain control challenges
Genetics not well established
Definitions
NF2 = inherited syndrome with multiple schwannomas,meningiomas, &ependymomas
Batchala PP et al: Imaging of tumor syndromes. Radiol Clin North Am. 59(3):471-500, 2021
Ren Y et al: New developments in neurofibromatosis type 2 and vestibular schwannoma. Neurooncol Adv. 3(1):vdaa153, 2021
Slattery WH: Neurofibromatosis type 2. Otolaryngol Clin North Am. 48(3):443-60, 2015
Maniakas A et al: Neurofibromatosis type 2 vestibular schwannoma treatment: a review of the literature, trends, and outcomes. Otol Neurotol. 35(5):889-94, 2014
Koontz NA et al: Schwannomatosis: the overlooked neurofibromatosis? AJR Am J Roentgenol. 200(6):W646-53, 2013
Sughrue ME et al: A prospective study of hearing preservation in untreated vestibular schwannomas. J Neurosurg. 114(2):381-5, 2011
Hsu PW et al: Outcomes of 75 patients over 12 years treated for acoustic neuromas with linear accelerator-based radiosurgery. J Clin Neurosci. 17(5):556-60, 2010
Kissil JL et al: What's new in neurofibromatosis? Proceedings from the 2009 NF Conference: new frontiers. Am J Med Genet A. 152A(2):269-83, 2010
Mautner VF et al: Bevacizumab induces regression of vestibular schwannomas in patients with neurofibromatosis type 2. Neuro Oncol. 12(1):14-8, 2010
Suryanarayanan R et al: Vestibular schwannoma: role of conservative management. J Laryngol Otol. 124(3):251-7, 2010
Fisher LM et al: Concordance of bilateral vestibular schwannoma growth and hearing changes in neurofibromatosis 2: neurofibromatosis 2 natural history consortium. Otol Neurotol. 30(6):835-41, 2009
Plotkin SR et al: Hearing improvement after bevacizumab in patients with neurofibromatosis type 2. N Engl J Med. 361(4):358-67, 2009
Moffat DA et al: Management strategies in neurofibromatosis type 2. Eur Arch Otorhinolaryngol. 260(1):12-8, 2003
Brackmann DE et al: Early proactive management of vestibular schwannomas in neurofibromatosis type 2. Neurosurgery. 49(2):274-80; discussion 280-3, 2001
Gillespie JE: Imaging in neurofibromatosis type 2: screening using magnetic resonance imaging. Ear Nose Throat J. 78(2):102-3, 106, 108-9, 1999
Kiroğlu MM et al: Bilateral acoustic neurofibromatosis with bilateral multicentric facial schwannomas. Eur Arch Otorhinolaryngol. 253(4-5):305-8, 1996
Akeson P et al: Radiological investigation of neurofibromatosis type 2. Neuroradiology. 36(2):107-10, 1994
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