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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Oval window atresia (OWA)
Synonyms
- Congenital absence of oval window (OW)
Definitions
- Absent space between lateral semicircular canal above and cochlear promontory below
- Associated with anomalous stapes and malpositioned CNVII
- Normal OW: Stapes footplate + annular ligament
IMAGING
General Features
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Vincent R et al: Congenital oval or round window malformations in children: Surgical findings and results in 17 cases. Laryngoscope. 126(11):2552-58, 2016
- Zhao S et al: Round window application of an active middle ear implant (AMEI) system in congenital oval window atresia. Acta Otolaryngol. 136(1):23-33, 2016
- Colletti L et al: Vestibulotomy with ossiculoplasty versus round window vibroplasty procedure in children with oval window aplasia. Otol Neurotol. 35(5):831-7, 2014
- Sennaroğlu L et al: Oval window atresia: a novel surgical approach and pathognomonic radiological finding. Int J Pediatr Otorhinolaryngol. 78(5):769-76, 2014
- Su Y et al: Congenital middle ear abnormalities with absence of the oval window: diagnosis, surgery, and audiometric outcomes. Otol Neurotol. 35(7):1191-5, 2014
- Ukkola-Pons E et al: Oval window niche height: quantitative evaluation with CT before stapes surgery for otosclerosis. AJNR Am J Neuroradiol. 34(5):1082-5, 2013
- de Alarcon A et al: Congenital absence of the oval window: diagnosis, surgery, and audiometric outcomes. Otol Neurotol. 29(1):23-8, 2008
- Martin C et al: Abnormal facial nerve course associated with stapes fixation or oval window absence: report of two cases. Eur Arch Otorhinolaryngol. 263(1):79-85, 2006
- Booth TN et al: Imaging and clinical evaluation of isolated atresia of the oval window. AJNR Am J Neuroradiol. 21(1):171-4, 2000
- Zeifer B et al: Congenital absence of the oval window: radiologic diagnosis and associated anomalies. AJNR Am J Neuroradiol. 21(2):322-7, 2000
- Lambert PR: Congenital absence of the oval window. Laryngoscope. 100(1):37-40, 1990
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Oval window atresia (OWA)
Synonyms
- Congenital absence of oval window (OW)
Definitions
- Absent space between lateral semicircular canal above and cochlear promontory below
- Associated with anomalous stapes and malpositioned CNVII
- Normal OW: Stapes footplate + annular ligament
IMAGING
General Features
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Vincent R et al: Congenital oval or round window malformations in children: Surgical findings and results in 17 cases. Laryngoscope. 126(11):2552-58, 2016
- Zhao S et al: Round window application of an active middle ear implant (AMEI) system in congenital oval window atresia. Acta Otolaryngol. 136(1):23-33, 2016
- Colletti L et al: Vestibulotomy with ossiculoplasty versus round window vibroplasty procedure in children with oval window aplasia. Otol Neurotol. 35(5):831-7, 2014
- Sennaroğlu L et al: Oval window atresia: a novel surgical approach and pathognomonic radiological finding. Int J Pediatr Otorhinolaryngol. 78(5):769-76, 2014
- Su Y et al: Congenital middle ear abnormalities with absence of the oval window: diagnosis, surgery, and audiometric outcomes. Otol Neurotol. 35(7):1191-5, 2014
- Ukkola-Pons E et al: Oval window niche height: quantitative evaluation with CT before stapes surgery for otosclerosis. AJNR Am J Neuroradiol. 34(5):1082-5, 2013
- de Alarcon A et al: Congenital absence of the oval window: diagnosis, surgery, and audiometric outcomes. Otol Neurotol. 29(1):23-8, 2008
- Martin C et al: Abnormal facial nerve course associated with stapes fixation or oval window absence: report of two cases. Eur Arch Otorhinolaryngol. 263(1):79-85, 2006
- Booth TN et al: Imaging and clinical evaluation of isolated atresia of the oval window. AJNR Am J Neuroradiol. 21(1):171-4, 2000
- Zeifer B et al: Congenital absence of the oval window: radiologic diagnosis and associated anomalies. AJNR Am J Neuroradiol. 21(2):322-7, 2000
- Lambert PR: Congenital absence of the oval window. Laryngoscope. 100(1):37-40, 1990
