Primary exocrine epithelial malignancy of pancreas occurring in young children
IMAGING
General Features
Ultrasonographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Qiu L et al: Pancreatic masses in children and young adults: multimodality review with pathologic correlation. Radiographics. 41(6):1766-84, 2021
Yang Z et al: Differential diagnosis of pancreatoblastoma (PB) and solid pseudopapillary neoplasms (SPNs) in children by CT and MR imaging. Eur Radiol. 31(4):2209-27, 2020
Huang Y et al: Diagnosis and treatment of pancreatoblastoma in children: a retrospective study in a single pediatric center. Pediatr Surg Int. 35(11):1231-8, 2019
Mylonas KS et al: Solid pseudopapillary and malignant pancreatic tumors in childhood: a systematic review and evidence quality assessment. Pediatr Blood Cancer. 65(10):e27114, 2018
Shet NS et al: Imaging of pediatric pancreatic neoplasms with radiologic-histopathologic correlation. AJR Am J Roentgenol. 202(6):1337-48, 2014
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TERMINOLOGY
Definitions
Primary exocrine epithelial malignancy of pancreas occurring in young children
IMAGING
General Features
Ultrasonographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Qiu L et al: Pancreatic masses in children and young adults: multimodality review with pathologic correlation. Radiographics. 41(6):1766-84, 2021
Yang Z et al: Differential diagnosis of pancreatoblastoma (PB) and solid pseudopapillary neoplasms (SPNs) in children by CT and MR imaging. Eur Radiol. 31(4):2209-27, 2020
Huang Y et al: Diagnosis and treatment of pancreatoblastoma in children: a retrospective study in a single pediatric center. Pediatr Surg Int. 35(11):1231-8, 2019
Mylonas KS et al: Solid pseudopapillary and malignant pancreatic tumors in childhood: a systematic review and evidence quality assessment. Pediatr Blood Cancer. 65(10):e27114, 2018
Shet NS et al: Imaging of pediatric pancreatic neoplasms with radiologic-histopathologic correlation. AJR Am J Roentgenol. 202(6):1337-48, 2014
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