Pneumatosis intestinalis; pneumatosis coli (confined to colon); pneumatosis cystoides intestinalis
Definitions
Presence of gas within walls of gastrointestinal tract
Associated with necrotizing enterocolitis in
Premature infants
Term newborns with congenital heart disease & other cardiovascular abnormalities
In older children, more frequently benign & associated with variety of underlying conditions & medications
IMAGING
General Features
Radiographic Findings
CT Findings
Ultrasonographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Treatment
Selected References
Ryan JL et al: Conservative management of pneumatosis intestinalis and portal venous gas after pediatric liver transplantation. Transplant Proc. 52(3):938-42, 2020
Chang CY et al: Benign pneumatosis intestinalis in a pediatric patient with multiple risk factors including granulomatosis with polyangiitis: a case report and review of the literature. Semin Arthritis Rheum. 44(4):423-7, 2015
Gui X et al: Is pneumatosis cystoides intestinalis gas-distended and ruptured lymphatics? Reappraisal by immunohistochemistry. Arch Pathol Lab Med. 138(8):1059-66, 2014
Lee KS et al: Distinguishing benign and life-threatening pneumatosis intestinalis in patients with cancer by CT imaging features. AJR Am J Roentgenol. 200(5):1042-7, 2013
Korhonen K et al: Incidence, risk factors, and outcome of pneumatosis intestinalis in pediatric stem cell transplant recipients. Pediatr Blood Cancer. 58(4):616-20, 2012
Duron VP et al: Computed tomographic diagnosis of pneumatosis intestinalis: clinical measures predictive of the need for surgical intervention. Arch Surg. 146(5):506-10, 2011
Li S et al: Pneumatosis intestinalis in children with acute lymphoblastic leukemia and acute myeloid leukemia. Support Care Cancer. 20(2):343-7, 2011
Olson DE et al: CT predictors for differentiating benign and clinically worrisome pneumatosis intestinalis in children beyond the neonatal period. Radiology. 253(2):513-9, 2009
McCarville MB et al: Clinical and CT features of benign pneumatosis intestinalis in pediatric hematopoietic stem cell transplant and oncology patients. Pediatr Radiol. 38(10):1074-83, 2008
Ho LM et al: Pneumatosis intestinalis in the adult: benign to life-threatening causes. AJR Am J Roentgenol. 188(6):1604-13, 2007
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References
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Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
Pneumatosis intestinalis; pneumatosis coli (confined to colon); pneumatosis cystoides intestinalis
Definitions
Presence of gas within walls of gastrointestinal tract
Associated with necrotizing enterocolitis in
Premature infants
Term newborns with congenital heart disease & other cardiovascular abnormalities
In older children, more frequently benign & associated with variety of underlying conditions & medications
IMAGING
General Features
Radiographic Findings
CT Findings
Ultrasonographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Treatment
Selected References
Ryan JL et al: Conservative management of pneumatosis intestinalis and portal venous gas after pediatric liver transplantation. Transplant Proc. 52(3):938-42, 2020
Chang CY et al: Benign pneumatosis intestinalis in a pediatric patient with multiple risk factors including granulomatosis with polyangiitis: a case report and review of the literature. Semin Arthritis Rheum. 44(4):423-7, 2015
Gui X et al: Is pneumatosis cystoides intestinalis gas-distended and ruptured lymphatics? Reappraisal by immunohistochemistry. Arch Pathol Lab Med. 138(8):1059-66, 2014
Lee KS et al: Distinguishing benign and life-threatening pneumatosis intestinalis in patients with cancer by CT imaging features. AJR Am J Roentgenol. 200(5):1042-7, 2013
Korhonen K et al: Incidence, risk factors, and outcome of pneumatosis intestinalis in pediatric stem cell transplant recipients. Pediatr Blood Cancer. 58(4):616-20, 2012
Duron VP et al: Computed tomographic diagnosis of pneumatosis intestinalis: clinical measures predictive of the need for surgical intervention. Arch Surg. 146(5):506-10, 2011
Li S et al: Pneumatosis intestinalis in children with acute lymphoblastic leukemia and acute myeloid leukemia. Support Care Cancer. 20(2):343-7, 2011
Olson DE et al: CT predictors for differentiating benign and clinically worrisome pneumatosis intestinalis in children beyond the neonatal period. Radiology. 253(2):513-9, 2009
McCarville MB et al: Clinical and CT features of benign pneumatosis intestinalis in pediatric hematopoietic stem cell transplant and oncology patients. Pediatr Radiol. 38(10):1074-83, 2008
Ho LM et al: Pneumatosis intestinalis in the adult: benign to life-threatening causes. AJR Am J Roentgenol. 188(6):1604-13, 2007
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