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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
Pneumatosis intestinalis; pneumatosis coli (confined to colon); pneumatosis cystoides intestinalis
Definitions
Presence of gas within walls of GI tract
Associated with necrotizing enterocolitis in
Premature infants
Term newborns with
Congenital heart disease
Hirschsprung disease
Maternal use of vasoconstrictive agents (e.g., cocaine)
In older children, more frequently benign & associated with variety of underlying conditions & medications
IMAGING
General Features
Radiographic Findings
CT Findings
Ultrasonographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Treatment
Selected References
Chang CY et al: Benign pneumatosis intestinalis in a pediatric patient with multiple risk factors including granulomatosis with polyangiitis: a case report and review of the literature. Semin Arthritis Rheum. 44(4):423-7, 2015
Gui X et al: Is pneumatosis cystoides intestinalis gas-distended and ruptured lymphatics? Reappraisal by immunohistochemistry. Arch Pathol Lab Med. 138(8):1059-66, 2014
Lee KS et al: Distinguishing benign and life-threatening pneumatosis intestinalis in patients with cancer by CT imaging features. AJR Am J Roentgenol. 200(5):1042-7, 2013
Korhonen K et al: Incidence, risk factors, and outcome of pneumatosis intestinalis in pediatric stem cell transplant recipients. Pediatr Blood Cancer. 58(4):616-20, 2012
Duron VP et al: Computed tomographic diagnosis of pneumatosis intestinalis: clinical measures predictive of the need for surgical intervention. Arch Surg. 146(5):506-10, 2011
Li S et al: Pneumatosis intestinalis in children with acute lymphoblastic leukemia and acute myeloid leukemia. Support Care Cancer. Epub ahead of print, 2011
Olson DE et al: CT predictors for differentiating benign and clinically worrisome pneumatosis intestinalis in children beyond the neonatal period. Radiology. 253(2):513-9, 2009
McCarville MB et al: Clinical and CT features of benign pneumatosis intestinalis in pediatric hematopoietic stem cell transplant and oncology patients. Pediatr Radiol. 38(10):1074-83, 2008
Ho LM et al: Pneumatosis intestinalis in the adult: benign to life-threatening causes. AJR Am J Roentgenol. 188(6):1604-13, 2007
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Synonyms
Pneumatosis intestinalis; pneumatosis coli (confined to colon); pneumatosis cystoides intestinalis
Definitions
Presence of gas within walls of GI tract
Associated with necrotizing enterocolitis in
Premature infants
Term newborns with
Congenital heart disease
Hirschsprung disease
Maternal use of vasoconstrictive agents (e.g., cocaine)
In older children, more frequently benign & associated with variety of underlying conditions & medications
IMAGING
General Features
Radiographic Findings
CT Findings
Ultrasonographic Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Treatment
Selected References
Chang CY et al: Benign pneumatosis intestinalis in a pediatric patient with multiple risk factors including granulomatosis with polyangiitis: a case report and review of the literature. Semin Arthritis Rheum. 44(4):423-7, 2015
Gui X et al: Is pneumatosis cystoides intestinalis gas-distended and ruptured lymphatics? Reappraisal by immunohistochemistry. Arch Pathol Lab Med. 138(8):1059-66, 2014
Lee KS et al: Distinguishing benign and life-threatening pneumatosis intestinalis in patients with cancer by CT imaging features. AJR Am J Roentgenol. 200(5):1042-7, 2013
Korhonen K et al: Incidence, risk factors, and outcome of pneumatosis intestinalis in pediatric stem cell transplant recipients. Pediatr Blood Cancer. 58(4):616-20, 2012
Duron VP et al: Computed tomographic diagnosis of pneumatosis intestinalis: clinical measures predictive of the need for surgical intervention. Arch Surg. 146(5):506-10, 2011
Li S et al: Pneumatosis intestinalis in children with acute lymphoblastic leukemia and acute myeloid leukemia. Support Care Cancer. Epub ahead of print, 2011
Olson DE et al: CT predictors for differentiating benign and clinically worrisome pneumatosis intestinalis in children beyond the neonatal period. Radiology. 253(2):513-9, 2009
McCarville MB et al: Clinical and CT features of benign pneumatosis intestinalis in pediatric hematopoietic stem cell transplant and oncology patients. Pediatr Radiol. 38(10):1074-83, 2008
Ho LM et al: Pneumatosis intestinalis in the adult: benign to life-threatening causes. AJR Am J Roentgenol. 188(6):1604-13, 2007
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