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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Polymyositis/dermatomyositis (P/D)
Synonyms
P/D interstitial lung disease (ILD)
Idiopathic inflammatory myopathy ILD
Definitions
Autoimmune myopathy
Manifests with inflammation and weakness
Dermatomyositis exhibits variety of cutaneous manifestations
Polymyositis involves proximal muscles over weeks or months
May be complicated by connective tissue disease-associated ILD (CTD-ILD), aspiration bronchiolitis, &/or hypoventilation from affected respiratory muscles
CTD-ILD: Diffuse interstitial pneumonia secondary to P/D
Aspiration bronchiolitis: Typically diffuse
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Elicker BM et al: Imaging of the thoracic manifestations of connective tissue disease. Clin Chest Med. 40(3):655-66, 2019
Kusmirek JE et al: Thoracic manifestations of connective tissue diseases. Semin Ultrasound CT MR. 40(3):239-54, 2019
Ahuja J et al: Imaging of pulmonary manifestations of connective tissue diseases. Radiol Clin North Am. 54(6):1015-31, 2016
Wang H et al: Pulmonary hypertension in polymyositis. Clin Rheumatol. 34(12):2105-12, 2015
Tanizawa K et al: The prognostic value of HRCT in myositis-associated interstitial lung disease. Respir Med. 107(5):745-52, 2013
Hervier B et al: Clinical manifestations of anti-synthetase syndrome positive for anti-alanyl-tRNA synthetase (anti-PL12) antibodies: a retrospective study of 17 cases. Rheumatology (Oxford). 49(5):972-6, 2010
Chen IJ et al: Interstitial lung disease in polymyositis and dermatomyositis. Clin Rheumatol. 28(6):639-46, 2009
Kang EH et al: Interstitial lung disease in patients with polymyositis, dermatomyositis and amyopathic dermatomyositis. Rheumatology (Oxford). 44(10):1282-6, 2005
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Polymyositis/dermatomyositis (P/D)
Synonyms
P/D interstitial lung disease (ILD)
Idiopathic inflammatory myopathy ILD
Definitions
Autoimmune myopathy
Manifests with inflammation and weakness
Dermatomyositis exhibits variety of cutaneous manifestations
Polymyositis involves proximal muscles over weeks or months
May be complicated by connective tissue disease-associated ILD (CTD-ILD), aspiration bronchiolitis, &/or hypoventilation from affected respiratory muscles
CTD-ILD: Diffuse interstitial pneumonia secondary to P/D
Aspiration bronchiolitis: Typically diffuse
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Elicker BM et al: Imaging of the thoracic manifestations of connective tissue disease. Clin Chest Med. 40(3):655-66, 2019
Kusmirek JE et al: Thoracic manifestations of connective tissue diseases. Semin Ultrasound CT MR. 40(3):239-54, 2019
Ahuja J et al: Imaging of pulmonary manifestations of connective tissue diseases. Radiol Clin North Am. 54(6):1015-31, 2016
Wang H et al: Pulmonary hypertension in polymyositis. Clin Rheumatol. 34(12):2105-12, 2015
Tanizawa K et al: The prognostic value of HRCT in myositis-associated interstitial lung disease. Respir Med. 107(5):745-52, 2013
Hervier B et al: Clinical manifestations of anti-synthetase syndrome positive for anti-alanyl-tRNA synthetase (anti-PL12) antibodies: a retrospective study of 17 cases. Rheumatology (Oxford). 49(5):972-6, 2010
Chen IJ et al: Interstitial lung disease in polymyositis and dermatomyositis. Clin Rheumatol. 28(6):639-46, 2009
Kang EH et al: Interstitial lung disease in patients with polymyositis, dermatomyositis and amyopathic dermatomyositis. Rheumatology (Oxford). 44(10):1282-6, 2005
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