Rossi M et al: Looking for new anabolic treatment from rare diseases of bone formation. J Endocrinol. 248(2):R29-40, 2021
Ayyavoo A et al: Elimination of pain and improvement of exercise capacity in Camurati-Engelmann disease with losartan. J Clin Endocrinol Metab. 99(11):3978-82, 2014
Harisankar CN et al: Tc99m-MDP bone scintigraphy in Engelmann-Camurati disease. Indian J Nucl Med. 26(1):44-5, 2011
Ihde LL et al: Sclerosing bone dysplasias: review and differentiation from other causes of osteosclerosis. Radiographics. 31(7):1865-82, 2011
DamiĆ” Ade B et al: Bone scintigraphy in Engelmann-Camurati disease. Clin Nucl Med. 35(7):559-60, 2010
Bartuseviciene A et al: Camurati-Engelmann disease: imaging, clinical features and differential diagnosis. Skeletal Radiol. 38(11):1037-43, 2009
Janssens K et al: Camurati-Engelmann disease: review of the clinical, radiological, and molecular data of 24 families and implications for diagnosis and treatment. J Med Genet. 43(1):1-11, 2006
Kaftori JK et al: Progressive diaphyseal dysplasia (Camurati-Engelmann): radiographic follow-up and CT findings. Radiology. 164(3):777-82, 1987
Related Anatomy
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Progressive diaphyseal dysplasia (PDD)
Synonyms
Engelmann-Camurati disease (ECD)
Camurati-Engelmann disease/syndrome (CED)
Definitions
Belongs to group of craniotubular hyperostoses
Sclerosing bone dysplasia
IMAGING
General Features
Imaging Recommendations
Radiographic Findings
CT Findings
MR Findings
Nuclear Medicine Findings
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Rossi M et al: Looking for new anabolic treatment from rare diseases of bone formation. J Endocrinol. 248(2):R29-40, 2021
Ayyavoo A et al: Elimination of pain and improvement of exercise capacity in Camurati-Engelmann disease with losartan. J Clin Endocrinol Metab. 99(11):3978-82, 2014
Harisankar CN et al: Tc99m-MDP bone scintigraphy in Engelmann-Camurati disease. Indian J Nucl Med. 26(1):44-5, 2011
Ihde LL et al: Sclerosing bone dysplasias: review and differentiation from other causes of osteosclerosis. Radiographics. 31(7):1865-82, 2011
DamiĆ” Ade B et al: Bone scintigraphy in Engelmann-Camurati disease. Clin Nucl Med. 35(7):559-60, 2010
Bartuseviciene A et al: Camurati-Engelmann disease: imaging, clinical features and differential diagnosis. Skeletal Radiol. 38(11):1037-43, 2009
Janssens K et al: Camurati-Engelmann disease: review of the clinical, radiological, and molecular data of 24 families and implications for diagnosis and treatment. J Med Genet. 43(1):1-11, 2006
Kaftori JK et al: Progressive diaphyseal dysplasia (Camurati-Engelmann): radiographic follow-up and CT findings. Radiology. 164(3):777-82, 1987
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