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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Proximal interruption of pulmonary artery (PIPA)
Synonyms
- Unilateral absence of pulmonary artery (UAPA)
- "Interruption" preferred over "absence": Intact pulmonary trunk and contralateral pulmonary artery
- Unilateral absence of pulmonary artery (UAPA)
Definitions
- Failed development of proximal pulmonary artery
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Angiographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Natural History & Prognosis
Treatment
Selected References
- Leitman EM et al: Pulmonary arteries: imaging of pulmonary embolism and beyond. Cardiovasc Diagn Ther. 9(Suppl 1):S37-58, 2019
- Williams EA et al: Proximal interruption of the pulmonary artery. J Thorac Imaging. 34(1):56-64, 2019
- Dillman JR et al: Expanding upon the unilateral hyperlucent hemithorax in children. Radiographics. 31(3):723-41, 2011
- Lee EY et al: Multidetector CT evaluation of congenital lung anomalies. Radiology. 247(3):632-48, 2008
- Castañer E et al: Congenital and acquired pulmonary artery anomalies in the adult: radiologic overview. Radiographics. 26(2):349-71, 2006
- Newman B: Congenital bronchopulmonary foregut malformations: concepts and controversies. Pediatr Radiol. 36(8):773-91, 2006
- Ryu DS et al: HRCT findings of proximal interruption of the right pulmonary artery. J Thorac Imaging. 19(3):171-5, 2004
- Ten Harkel AD et al: Isolated unilateral absence of a pulmonary artery: a case report and review of the literature. Chest. 122(4):1471-7, 2002
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
- Proximal interruption of pulmonary artery (PIPA)
Synonyms
- Unilateral absence of pulmonary artery (UAPA)
- "Interruption" preferred over "absence": Intact pulmonary trunk and contralateral pulmonary artery
- Unilateral absence of pulmonary artery (UAPA)
Definitions
- Failed development of proximal pulmonary artery
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Angiographic Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
CLINICAL ISSUES
Presentation
Natural History & Prognosis
Treatment
Selected References
- Leitman EM et al: Pulmonary arteries: imaging of pulmonary embolism and beyond. Cardiovasc Diagn Ther. 9(Suppl 1):S37-58, 2019
- Williams EA et al: Proximal interruption of the pulmonary artery. J Thorac Imaging. 34(1):56-64, 2019
- Dillman JR et al: Expanding upon the unilateral hyperlucent hemithorax in children. Radiographics. 31(3):723-41, 2011
- Lee EY et al: Multidetector CT evaluation of congenital lung anomalies. Radiology. 247(3):632-48, 2008
- Castañer E et al: Congenital and acquired pulmonary artery anomalies in the adult: radiologic overview. Radiographics. 26(2):349-71, 2006
- Newman B: Congenital bronchopulmonary foregut malformations: concepts and controversies. Pediatr Radiol. 36(8):773-91, 2006
- Ryu DS et al: HRCT findings of proximal interruption of the right pulmonary artery. J Thorac Imaging. 19(3):171-5, 2004
- Ten Harkel AD et al: Isolated unilateral absence of a pulmonary artery: a case report and review of the literature. Chest. 122(4):1471-7, 2002
