link
Bookmarks
Pulmonary Agenesis
Emily Edwards, MD
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Subscribe
0
0
2
1

KEY FACTS

  • Imaging

    • Top Differential Diagnoses

      • Pathology

        • Clinical Issues

          • Diagnostic Checklist

            TERMINOLOGY

            • Definitions

              • Failure of lung tissue development
                • Unilateral > bilateral
                  • Bilateral agenesis incompatible with life 
                • Spectrum from hypoplasia → partial agenesis → complete agenesis 

            IMAGING

            • General Features

              • Ultrasonographic Findings

                • MR Findings

                  DIFFERENTIAL DIAGNOSIS

                    PATHOLOGY

                    • General Features

                      • Staging, Grading, & Classification

                        CLINICAL ISSUES

                        • Presentation

                          • Demographics

                            • Natural History & Prognosis

                              • Treatment

                                DIAGNOSTIC CHECKLIST

                                • Consider

                                  Selected References

                                  1. Nguyen LN et al: Bilateral pulmonary agenesis: a rare and unexpected finding in a newborn. AJP Rep. 6(2):e246-9, 2016
                                  2. Dinamarco PV et al: Pulmonary agenesis and respiratory failure in childhood. Autops Case Rep. 5(1):29-32, 2015
                                  3. Muensterer O et al: Pulmonary agenesis and associated pulmonary hypertension: a case report and review on variability, therapy, and outcome. European J Pediatr Surg Rep. 3(1):33-9, 2015
                                  4. Kayemba-Kay's S et al: Unilateral pulmonary agenesis: a report of four cases, two diagnosed antenatally and literature review. Pediatr Pulmonol. 49(3):E96-102, 2014
                                  5. Russell BC et al: Isolated unilateral pulmonary agenesis and other fetal thoracic anomalies. Obstet Gynecol Surv. 69(6):335-45, 2014
                                  6. Pacharn P et al: Congenital lung lesions: prenatal MRI and postnatal findings. Pediatr Radiol. 43(9):1136-43, 2013
                                  7. Meller CH et al: Prenatal diagnosis of isolated right pulmonary agenesis using sonography alone: case study and systematic literature review. J Ultrasound Med. 31(12):2017-23, 2012
                                  8. Gabarre JA et al: Isolated unilateral pulmonary agenesis: early prenatal diagnosis and long-term follow-up. J Ultrasound Med. 24(6):865-8, 2005
                                  9. Viora E et al: Prenatal diagnosis of isolated unilateral pulmonary agenesis in the second trimester. Ultrasound Obstet Gynecol. 19(2):206-7, 2002
                                  10. Nowotny T et al: Right-sided pulmonary aplasia: longitudinal lung function studies in two cases and comparison to results from term healthy neonates. Pediatr Pulmonol. 26(2):138-44, 1998
                                  11. Kalache KD et al: Prenatal diagnosis of right lung agenesis using color Doppler and magnetic resonance imaging. Fetal Diagn Ther. 12(6):360-2, 1997
                                  Related Anatomy
                                  Loading...
                                  Related Differential Diagnoses
                                  Loading...
                                  References
                                  Tables

                                  Tables

                                  KEY FACTS

                                  • Imaging

                                    • Top Differential Diagnoses

                                      • Pathology

                                        • Clinical Issues

                                          • Diagnostic Checklist

                                            TERMINOLOGY

                                            • Definitions

                                              • Failure of lung tissue development
                                                • Unilateral > bilateral
                                                  • Bilateral agenesis incompatible with life 
                                                • Spectrum from hypoplasia → partial agenesis → complete agenesis 

                                            IMAGING

                                            • General Features

                                              • Ultrasonographic Findings

                                                • MR Findings

                                                  DIFFERENTIAL DIAGNOSIS

                                                    PATHOLOGY

                                                    • General Features

                                                      • Staging, Grading, & Classification

                                                        CLINICAL ISSUES

                                                        • Presentation

                                                          • Demographics

                                                            • Natural History & Prognosis

                                                              • Treatment

                                                                DIAGNOSTIC CHECKLIST

                                                                • Consider

                                                                  Selected References

                                                                  1. Nguyen LN et al: Bilateral pulmonary agenesis: a rare and unexpected finding in a newborn. AJP Rep. 6(2):e246-9, 2016
                                                                  2. Dinamarco PV et al: Pulmonary agenesis and respiratory failure in childhood. Autops Case Rep. 5(1):29-32, 2015
                                                                  3. Muensterer O et al: Pulmonary agenesis and associated pulmonary hypertension: a case report and review on variability, therapy, and outcome. European J Pediatr Surg Rep. 3(1):33-9, 2015
                                                                  4. Kayemba-Kay's S et al: Unilateral pulmonary agenesis: a report of four cases, two diagnosed antenatally and literature review. Pediatr Pulmonol. 49(3):E96-102, 2014
                                                                  5. Russell BC et al: Isolated unilateral pulmonary agenesis and other fetal thoracic anomalies. Obstet Gynecol Surv. 69(6):335-45, 2014
                                                                  6. Pacharn P et al: Congenital lung lesions: prenatal MRI and postnatal findings. Pediatr Radiol. 43(9):1136-43, 2013
                                                                  7. Meller CH et al: Prenatal diagnosis of isolated right pulmonary agenesis using sonography alone: case study and systematic literature review. J Ultrasound Med. 31(12):2017-23, 2012
                                                                  8. Gabarre JA et al: Isolated unilateral pulmonary agenesis: early prenatal diagnosis and long-term follow-up. J Ultrasound Med. 24(6):865-8, 2005
                                                                  9. Viora E et al: Prenatal diagnosis of isolated unilateral pulmonary agenesis in the second trimester. Ultrasound Obstet Gynecol. 19(2):206-7, 2002
                                                                  10. Nowotny T et al: Right-sided pulmonary aplasia: longitudinal lung function studies in two cases and comparison to results from term healthy neonates. Pediatr Pulmonol. 26(2):138-44, 1998
                                                                  11. Kalache KD et al: Prenatal diagnosis of right lung agenesis using color Doppler and magnetic resonance imaging. Fetal Diagn Ther. 12(6):360-2, 1997