Upper respiratory tract, pulmonary, and renal involvement
IMAGING
General Features
Radiographic Findings
CT Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Diagnosis
Treatment
Natural History & Prognosis
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Almaani S et al: ANCA-associated vasculitis: an update. J Clin Med. 10(7), 2021
Selvaraj V et al: COVID-19-induced granulomatosis with polyangiitis. BMJ Case Rep. 14(3), 2021
Sun X et al: Clinical features and long-term outcomes of interstitial lung disease with anti-neutrophil cytoplasmic antibody. BMC Pulm Med. 21(1):88, 2021
Zhou P et al: Impact of interstitial lung disease on mortality in ANCA-associated vasculitis: A systematic literature review and meta-analysis. Chron Respir Dis. 18:1479973121994562, 2021
Lawton A et al: Pulmonary manifestations of systemic vasculitis in childhood. Breathe (Sheff). 16(4):200211, 2020
Broncano J et al: CT and MR imaging of cardiothoracic vasculitis. Radiographics. 38(4):997-1021, 2018
Feragalli B et al: The lung in systemic vasculitis: radiological patterns and differential diagnosis. Br J Radiol. 89(1061):20150992, 2016
Hasleton P et al: Pulmonary vasculitis and pulmonary hemorrhage syndromes. In Spencer's Pathology of the Lung. 6th ed. Cambridge University Press. 713-29, 2013
Martinez F et al: Common and uncommon manifestations of Wegener granulomatosis at chest CT: radiologic-pathologic correlation. Radiographics. 32(1):51-69, 2012
CastaƱer E et al: When to suspect pulmonary vasculitis: radiologic and clinical clues. Radiographics. 30(1):33-53, 2010
Ananthakrishnan L et al: Wegener's granulomatosis in the chest: high-resolution CT findings. AJR Am J Roentgenol. 192(3):676-82, 2009
Lohrmann C et al: Pulmonary manifestations of wegener granulomatosis: CT findings in 57 patients and a review of the literature. Eur J Radiol. 53(3):471-7, 2005
Sheehan RE et al: Computed tomography features of the thoracic manifestations of Wegener granulomatosis. J Thorac Imaging. 18(1):34-41, 2003
Frazier AA et al: Pulmonary angiitis and granulomatosis: radiologic-pathologic correlation. Radiographics. 18(3):687-710; quiz 727, 1998
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Wegener granulomatosis: Term no longer in use
Synonyms
Granulomatosis and polyangiitis (GPA)
Definitions
Multisystem necrotizing granulomatous vasculitis of small to medium-sized blood vessels (arteries, capillaries, veins)
Upper respiratory tract, pulmonary, and renal involvement
IMAGING
General Features
Radiographic Findings
CT Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Diagnosis
Treatment
Natural History & Prognosis
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Almaani S et al: ANCA-associated vasculitis: an update. J Clin Med. 10(7), 2021
Selvaraj V et al: COVID-19-induced granulomatosis with polyangiitis. BMJ Case Rep. 14(3), 2021
Sun X et al: Clinical features and long-term outcomes of interstitial lung disease with anti-neutrophil cytoplasmic antibody. BMC Pulm Med. 21(1):88, 2021
Zhou P et al: Impact of interstitial lung disease on mortality in ANCA-associated vasculitis: A systematic literature review and meta-analysis. Chron Respir Dis. 18:1479973121994562, 2021
Lawton A et al: Pulmonary manifestations of systemic vasculitis in childhood. Breathe (Sheff). 16(4):200211, 2020
Broncano J et al: CT and MR imaging of cardiothoracic vasculitis. Radiographics. 38(4):997-1021, 2018
Feragalli B et al: The lung in systemic vasculitis: radiological patterns and differential diagnosis. Br J Radiol. 89(1061):20150992, 2016
Hasleton P et al: Pulmonary vasculitis and pulmonary hemorrhage syndromes. In Spencer's Pathology of the Lung. 6th ed. Cambridge University Press. 713-29, 2013
Martinez F et al: Common and uncommon manifestations of Wegener granulomatosis at chest CT: radiologic-pathologic correlation. Radiographics. 32(1):51-69, 2012
CastaƱer E et al: When to suspect pulmonary vasculitis: radiologic and clinical clues. Radiographics. 30(1):33-53, 2010
Ananthakrishnan L et al: Wegener's granulomatosis in the chest: high-resolution CT findings. AJR Am J Roentgenol. 192(3):676-82, 2009
Lohrmann C et al: Pulmonary manifestations of wegener granulomatosis: CT findings in 57 patients and a review of the literature. Eur J Radiol. 53(3):471-7, 2005
Sheehan RE et al: Computed tomography features of the thoracic manifestations of Wegener granulomatosis. J Thorac Imaging. 18(1):34-41, 2003
Frazier AA et al: Pulmonary angiitis and granulomatosis: radiologic-pathologic correlation. Radiographics. 18(3):687-710; quiz 727, 1998
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