Bookmarks
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Pulmonary venoocclusive disease (PVOD), pulmonary capillary hemangiomatosis (PCH)
Definitions
- Rare causes of pulmonary artery hypertension (PAH) (WHO Group 1)
- PVOD: Fibrous intimal proliferation and occlusion of pulmonary venules and small veins
- PCH: Proliferation of capillaries within alveolar walls
- PVOD and PCH are considered to be common entity and represent varied expressions of same disease
- Postcapillary pathologies; behave similar to precapillary PAH
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Reporting Tips
Selected References
- Galiè N et al: 2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension: The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS): Endorsed by: Association for European Paediatric and Congenital Cardiology (AEPC), International Society for Heart and Lung Transplantation (ISHLT). Eur Heart J. 37(1):67-119, 2016
- Montani D et al: Pulmonary veno-occlusive disease. Eur Respir J. 47(5):1518-34, 2016
- Huertas A et al: Pulmonary veno-occlusive disease: advances in clinical management and treatments. Expert Rev Respir Med. 5(2):217-29; quiz 230-1, 2011
- Montani D et al: Pulmonary veno-occlusive disease: recent progress and current challenges. Respir Med. 104 Suppl 1:S23-32, 2010
- Iwaki M et al: Idiopathic pulmonary veno-occlusive disease. Intern Med. 48(15):1289-92, 2009
- Montani D et al: Idiopathic pulmonary arterial hypertension and pulmonary veno-occlusive disease: similarities and differences. Semin Respir Crit Care Med. 30(4):411-20, 2009
- Montani D et al: Pulmonary veno-occlusive disease. Eur Respir J. 33(1):189-200, 2009
- Frazier AA et al: From the Archives of the AFIP: pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis. Radiographics. 27(3):867-82, 2007
- Resten A et al: CT imaging of peripheral pulmonary vessel disease. Eur Radiol. 15(10):2045-56, 2005
- Resten A et al: Pulmonary hypertension: CT of the chest in pulmonary venoocclusive disease. AJR Am J Roentgenol. 183(1):65-70, 2004
- Swensen SJ et al: Pulmonary venoocclusive disease: CT findings in eight patients. AJR Am J Roentgenol. 167(4):937-40, 1996
- Hasleton PS et al: Pulmonary veno-occlusive disease. A report of four cases. Histopathology. 10(9):933-44, 1986
Related Anatomy
Loading...
Related Differential Diagnoses
Loading...
References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Pulmonary venoocclusive disease (PVOD), pulmonary capillary hemangiomatosis (PCH)
Definitions
- Rare causes of pulmonary artery hypertension (PAH) (WHO Group 1)
- PVOD: Fibrous intimal proliferation and occlusion of pulmonary venules and small veins
- PCH: Proliferation of capillaries within alveolar walls
- PVOD and PCH are considered to be common entity and represent varied expressions of same disease
- Postcapillary pathologies; behave similar to precapillary PAH
IMAGING
General Features
Radiographic Findings
CT Findings
MR Findings
Echocardiographic Findings
Angiographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Reporting Tips
Selected References
- Galiè N et al: 2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension: The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS): Endorsed by: Association for European Paediatric and Congenital Cardiology (AEPC), International Society for Heart and Lung Transplantation (ISHLT). Eur Heart J. 37(1):67-119, 2016
- Montani D et al: Pulmonary veno-occlusive disease. Eur Respir J. 47(5):1518-34, 2016
- Huertas A et al: Pulmonary veno-occlusive disease: advances in clinical management and treatments. Expert Rev Respir Med. 5(2):217-29; quiz 230-1, 2011
- Montani D et al: Pulmonary veno-occlusive disease: recent progress and current challenges. Respir Med. 104 Suppl 1:S23-32, 2010
- Iwaki M et al: Idiopathic pulmonary veno-occlusive disease. Intern Med. 48(15):1289-92, 2009
- Montani D et al: Idiopathic pulmonary arterial hypertension and pulmonary veno-occlusive disease: similarities and differences. Semin Respir Crit Care Med. 30(4):411-20, 2009
- Montani D et al: Pulmonary veno-occlusive disease. Eur Respir J. 33(1):189-200, 2009
- Frazier AA et al: From the Archives of the AFIP: pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis. Radiographics. 27(3):867-82, 2007
- Resten A et al: CT imaging of peripheral pulmonary vessel disease. Eur Radiol. 15(10):2045-56, 2005
- Resten A et al: Pulmonary hypertension: CT of the chest in pulmonary venoocclusive disease. AJR Am J Roentgenol. 183(1):65-70, 2004
- Swensen SJ et al: Pulmonary venoocclusive disease: CT findings in eight patients. AJR Am J Roentgenol. 167(4):937-40, 1996
- Hasleton PS et al: Pulmonary veno-occlusive disease. A report of four cases. Histopathology. 10(9):933-44, 1986
