Bookmarks
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Rasmussen encephalitis (RE)
Synonyms
- Chronic focal (localized) encephalitis
Definitions
- Chronic, progressive, unilateral brain inflammation of uncertain etiology
- Characterized by hemispheric volume loss and difficulty controlling focal seizure activity
IMAGING
General Features
CT Findings
MR Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Foster MT et al: Motor cortex relocation after complete anatomical hemispherectomy for intractable epilepsy secondary to Rasmussen's encephalitis. Br J Neurosurg. 1-3, 2019
- Dupont S et al: Late-onset Rasmussen encephalitis: a literature appraisal. Autoimmun Rev. 16(8):803-10, 2017
- Gurcharran K et al: Anti-N-methyl-D-aspartate receptor encephalitis and Rasmussen-like syndrome: an association? Pediatr Neurol. 66:104-7, 2017
- Leypoldt F et al: Autoimmune encephalopathies. Ann N Y Acad Sci. 1338:94-114, 2014
- Press C et al: The Janus-faced nature of Rasmussen's encephalitis. Semin Pediatr Neurol. 21(2):129-36, 2014
- Varadkar S et al: Rasmussen's encephalitis: clinical features, pathobiology, and treatment advances. Lancet Neurol. 13(2):195-205, 2014
- Wang DD et al: Unilateral holohemispheric central nervous system lesions associated with medically refractory epilepsy in the pediatric population: a retrospective series of hemimegalencephaly and Rasmussen's encephalitis. J Neurosurg Pediatr. 1-12, 2014
- Nabbout R: Autoimmune and inflammatory epilepsies. Epilepsia. 53 Suppl 4:58-62, 2012
- Takei H et al: Dual pathology in Rasmussen's encephalitis: a study of seven cases and review of the literature. Neuropathology. 30(4):381-91, 2010
- Cauley KA et al: Diffusion tensor imaging and tractography of Rasmussen encephalitis. Pediatr Radiol. 39(7):727-30, 2009
- Faingold R et al: MRI appearance of Rasmussen encephalitis. Pediatr Radiol. 39(7):756, 2009
- Terra-Bustamante VC et al: Rasmussen encephalitis: long-term outcome after surgery. Childs Nerv Syst. 25(5):583-9, 2009
- Tessonnier L et al: Perfusion SPECT findings in a suspected case of Rasmussen encephalitis. J Neuroimaging. 19(4):378-80, 2009
- Misra UK et al: The prognostic role of magnetic resonance imaging and single-photon emission computed tomography in viral encephalitis. Acta Radiol. 49(7):827-32, 2008
- Cook SW et al: Cerebral hemispherectomy in pediatric patients with epilepsy: comparison of three techniques by pathological substrate in 115 patients. J Neurosurg. 100(2 Suppl Pediatrics):125-41, 2004
- Granata T et al: Experience with immunomodulatory treatments in Rasmussen's encephalitis. Neurology. 61(12):1807-10, 2003
- Maeda Y et al: Rasmussen syndrome: multifocal spread of inflammation suggested from MRI and PET findings. Epilepsia. 44(8):1118-21, 2003
- Bien CG et al: Diagnosis and staging of Rasmussen's encephalitis by serial MRI and histopathology. Neurology. 58(2):250-7, 2002
- Kim SJ et al: A longitudinal MRI study in children with Rasmussen syndrome. Pediatr Neurol. 27(4):282-8, 2002
- Fiorella DJ et al: (18)F-fluorodeoxyglucose positron emission tomography and MR imaging findings in Rasmussen encephalitis. AJNR Am J Neuroradiol. 22(7):1291-9, 2001
Related Anatomy
Loading...
Related Differential Diagnoses
Loading...
References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
- Rasmussen encephalitis (RE)
Synonyms
- Chronic focal (localized) encephalitis
Definitions
- Chronic, progressive, unilateral brain inflammation of uncertain etiology
- Characterized by hemispheric volume loss and difficulty controlling focal seizure activity
IMAGING
General Features
CT Findings
MR Findings
Nuclear Medicine Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Image Interpretation Pearls
Selected References
- Foster MT et al: Motor cortex relocation after complete anatomical hemispherectomy for intractable epilepsy secondary to Rasmussen's encephalitis. Br J Neurosurg. 1-3, 2019
- Dupont S et al: Late-onset Rasmussen encephalitis: a literature appraisal. Autoimmun Rev. 16(8):803-10, 2017
- Gurcharran K et al: Anti-N-methyl-D-aspartate receptor encephalitis and Rasmussen-like syndrome: an association? Pediatr Neurol. 66:104-7, 2017
- Leypoldt F et al: Autoimmune encephalopathies. Ann N Y Acad Sci. 1338:94-114, 2014
- Press C et al: The Janus-faced nature of Rasmussen's encephalitis. Semin Pediatr Neurol. 21(2):129-36, 2014
- Varadkar S et al: Rasmussen's encephalitis: clinical features, pathobiology, and treatment advances. Lancet Neurol. 13(2):195-205, 2014
- Wang DD et al: Unilateral holohemispheric central nervous system lesions associated with medically refractory epilepsy in the pediatric population: a retrospective series of hemimegalencephaly and Rasmussen's encephalitis. J Neurosurg Pediatr. 1-12, 2014
- Nabbout R: Autoimmune and inflammatory epilepsies. Epilepsia. 53 Suppl 4:58-62, 2012
- Takei H et al: Dual pathology in Rasmussen's encephalitis: a study of seven cases and review of the literature. Neuropathology. 30(4):381-91, 2010
- Cauley KA et al: Diffusion tensor imaging and tractography of Rasmussen encephalitis. Pediatr Radiol. 39(7):727-30, 2009
- Faingold R et al: MRI appearance of Rasmussen encephalitis. Pediatr Radiol. 39(7):756, 2009
- Terra-Bustamante VC et al: Rasmussen encephalitis: long-term outcome after surgery. Childs Nerv Syst. 25(5):583-9, 2009
- Tessonnier L et al: Perfusion SPECT findings in a suspected case of Rasmussen encephalitis. J Neuroimaging. 19(4):378-80, 2009
- Misra UK et al: The prognostic role of magnetic resonance imaging and single-photon emission computed tomography in viral encephalitis. Acta Radiol. 49(7):827-32, 2008
- Cook SW et al: Cerebral hemispherectomy in pediatric patients with epilepsy: comparison of three techniques by pathological substrate in 115 patients. J Neurosurg. 100(2 Suppl Pediatrics):125-41, 2004
- Granata T et al: Experience with immunomodulatory treatments in Rasmussen's encephalitis. Neurology. 61(12):1807-10, 2003
- Maeda Y et al: Rasmussen syndrome: multifocal spread of inflammation suggested from MRI and PET findings. Epilepsia. 44(8):1118-21, 2003
- Bien CG et al: Diagnosis and staging of Rasmussen's encephalitis by serial MRI and histopathology. Neurology. 58(2):250-7, 2002
- Kim SJ et al: A longitudinal MRI study in children with Rasmussen syndrome. Pediatr Neurol. 27(4):282-8, 2002
- Fiorella DJ et al: (18)F-fluorodeoxyglucose positron emission tomography and MR imaging findings in Rasmussen encephalitis. AJNR Am J Neuroradiol. 22(7):1291-9, 2001
