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KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Malignant rhabdoid tumor, extracranial rhabdoid tumor
Definitions
- Rare, highly aggressive neoplasm of young children with poor prognosis
- Most commonly occurs in kidney
IMAGING
General Features
Radiographic Findings
Ultrasonographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Nemes K et al: Clinical and genetic risk factors define two risk groups of extracranial malignant rhabdoid tumours (eMRT/RTK). Eur J Cancer. 142:112-22, 2021
- Treece AL: Pediatric renal tumors: updates in the molecular era. Surg Pathol Clin. 13(4):695-718, 2020
- Stanescu AL et al: Pediatric renal neoplasms: MR imaging-based practical diagnostic approach. Magn Reson Imaging Clin N Am. 27(2):279-90, 2019
- Chung EM et al: Renal tumors of childhood: radiologic-pathologic correlation part 1. The 1st decade: from the radiologic pathology archives. Radiographics. 36(2):499-522, 2016
- Farmakis SG et al: Rhabdoid tumor: an aggressive renal medullary tumor of childhood. J Comput Assist Tomogr. 39(1):44-6, 2015
- Hong CR et al: Extra-cranial malignant rhabdoid tumor in children: a single institute experience. Cancer Res Treat. 47(4):889-96, 2015
- Gee MS et al: Magnetic resonance imaging of the pediatric kidney: benign and malignant masses. Magn Reson Imaging Clin N Am. 21(4):697-715, 2013
- Royer-Pokora B: Genetics of pediatric renal tumors. Pediatr Nephrol. 28(1):13-23, 2013
- Geller E et al: Renal neoplasms of childhood. Radiol Clin North Am. 49(4):689-709, vi, 2011
- van den Heuvel-Eibrink MM et al: Malignant rhabdoid tumours of the kidney (MRTKs), registered on recent SIOP protocols from 1993 to 2005: a report of the SIOP renal tumour study group. Pediatr Blood Cancer. 56(5):733-7, 2011
- Morgenstern DA et al: Clinical and pathological features of paediatric malignant rhabdoid tumours. Pediatr Blood Cancer. 54(1):29-34, 2010
- Tomlinson GE et al: Rhabdoid tumor of the kidney in the National Wilms' Tumor Study: age at diagnosis as a prognostic factor. J Clin Oncol. 23(30):7641-5, 2005
- Agrons GA et al: Rhabdoid tumor of the kidney in children: a comparative study of 21 cases. AJR Am J Roentgenol. 168(2):447-51, 1997
- Nemes K et al: Rhabdoid tumor predisposition syndrome, 1993
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Synonyms
- Malignant rhabdoid tumor, extracranial rhabdoid tumor
Definitions
- Rare, highly aggressive neoplasm of young children with poor prognosis
- Most commonly occurs in kidney
IMAGING
General Features
Radiographic Findings
Ultrasonographic Findings
CT Findings
MR Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
- Nemes K et al: Clinical and genetic risk factors define two risk groups of extracranial malignant rhabdoid tumours (eMRT/RTK). Eur J Cancer. 142:112-22, 2021
- Treece AL: Pediatric renal tumors: updates in the molecular era. Surg Pathol Clin. 13(4):695-718, 2020
- Stanescu AL et al: Pediatric renal neoplasms: MR imaging-based practical diagnostic approach. Magn Reson Imaging Clin N Am. 27(2):279-90, 2019
- Chung EM et al: Renal tumors of childhood: radiologic-pathologic correlation part 1. The 1st decade: from the radiologic pathology archives. Radiographics. 36(2):499-522, 2016
- Farmakis SG et al: Rhabdoid tumor: an aggressive renal medullary tumor of childhood. J Comput Assist Tomogr. 39(1):44-6, 2015
- Hong CR et al: Extra-cranial malignant rhabdoid tumor in children: a single institute experience. Cancer Res Treat. 47(4):889-96, 2015
- Gee MS et al: Magnetic resonance imaging of the pediatric kidney: benign and malignant masses. Magn Reson Imaging Clin N Am. 21(4):697-715, 2013
- Royer-Pokora B: Genetics of pediatric renal tumors. Pediatr Nephrol. 28(1):13-23, 2013
- Geller E et al: Renal neoplasms of childhood. Radiol Clin North Am. 49(4):689-709, vi, 2011
- van den Heuvel-Eibrink MM et al: Malignant rhabdoid tumours of the kidney (MRTKs), registered on recent SIOP protocols from 1993 to 2005: a report of the SIOP renal tumour study group. Pediatr Blood Cancer. 56(5):733-7, 2011
- Morgenstern DA et al: Clinical and pathological features of paediatric malignant rhabdoid tumours. Pediatr Blood Cancer. 54(1):29-34, 2010
- Tomlinson GE et al: Rhabdoid tumor of the kidney in the National Wilms' Tumor Study: age at diagnosis as a prognostic factor. J Clin Oncol. 23(30):7641-5, 2005
- Agrons GA et al: Rhabdoid tumor of the kidney in children: a comparative study of 21 cases. AJR Am J Roentgenol. 168(2):447-51, 1997
- Nemes K et al: Rhabdoid tumor predisposition syndrome, 1993
