RB: Cellular bronchiolitis present in virtually all smokers, characterized by accumulation of pigmented macrophages in airways and alveoli
RB-ILD: Smoking-related ILD closely related to RB but with more severe histologic, imaging, and clinical features; RB causing symptoms and pulmonary function deficits
Spectrum of smoking-related ILD: RB, RB-ILD, and desquamative interstitial pneumonia (DIP)
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Diagnosis
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Sieminska A et al: Respiratory bronchiolitis-interstitial lung disease. Orphanet J Rare Dis. 9:106, 2014
Travis WD et al: An official American Thoracic Society/European Respiratory Society statement: update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med. 188(6):733-48, 2013
Attili AK et al: Smoking-related interstitial lung disease: radiologic-clinical-pathologic correlation. Radiographics. 28(5):1383-96; discussion 1396-8, 2008
Nakanishi M et al: Changes in HRCT findings in patients with respiratory bronchiolitis-associated interstitial lung disease after smoking cessation. Eur Respir J. 29(3):453-61, 2007
Fraig M et al: Respiratory bronchiolitis: a clinicopathologic study in current smokers, ex-smokers, and never-smokers. Am J Surg Pathol. 26(5):647-53, 2002
Park JS et al: Respiratory bronchiolitis-associated interstitial lung disease: radiologic features with clinical and pathologic correlation. J Comput Assist Tomogr. 26(1):13-20, 2002
RB: Cellular bronchiolitis present in virtually all smokers, characterized by accumulation of pigmented macrophages in airways and alveoli
RB-ILD: Smoking-related ILD closely related to RB but with more severe histologic, imaging, and clinical features; RB causing symptoms and pulmonary function deficits
Spectrum of smoking-related ILD: RB, RB-ILD, and desquamative interstitial pneumonia (DIP)
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Diagnosis
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Sieminska A et al: Respiratory bronchiolitis-interstitial lung disease. Orphanet J Rare Dis. 9:106, 2014
Travis WD et al: An official American Thoracic Society/European Respiratory Society statement: update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am J Respir Crit Care Med. 188(6):733-48, 2013
Attili AK et al: Smoking-related interstitial lung disease: radiologic-clinical-pathologic correlation. Radiographics. 28(5):1383-96; discussion 1396-8, 2008
Nakanishi M et al: Changes in HRCT findings in patients with respiratory bronchiolitis-associated interstitial lung disease after smoking cessation. Eur Respir J. 29(3):453-61, 2007
Fraig M et al: Respiratory bronchiolitis: a clinicopathologic study in current smokers, ex-smokers, and never-smokers. Am J Surg Pathol. 26(5):647-53, 2002
Park JS et al: Respiratory bronchiolitis-associated interstitial lung disease: radiologic features with clinical and pathologic correlation. J Comput Assist Tomogr. 26(1):13-20, 2002
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