link
Bookmarks
 (0)
Brain
Diagnosis
Pathology-Based Diagnoses
Stroke
Nonatheromatous Vasculopathy
Reversible Cerebral Vasoconstriction Syndrome
Reversible Cerebral Vasoconstriction Syndrome
Kelly A. Dahlstrom, DO; Karen L. Salzman, MD
To access 4,300 diagnoses written by the world's leading experts in radiology, please log in or subscribe.Log inSubscribe
0
3
1
0

KEY FACTS

  • Terminology

    • Imaging

      • Pathology

        • Clinical Issues

          TERMINOLOGY

          • Abbreviations

            • Reversible cerebral vasoconstriction syndrome (RCVS)

          • Synonyms

            • Call-Fleming syndrome

          • Definitions

            • Group of disorders characterized by
              • Reversible, multifocal cerebral artery vasoconstriction
              • Severe headaches (HAs) ± focal neurologic deficits

          IMAGING

          • General Features

            • CT Findings

              • MR Findings

                • Ultrasonographic Findings

                  • Angiographic Findings

                    DIFFERENTIAL DIAGNOSIS

                      PATHOLOGY

                      • General Features

                        CLINICAL ISSUES

                        • Presentation

                          • Natural History & Prognosis

                            • Treatment

                              DIAGNOSTIC CHECKLIST

                              • Consider

                                • Image Interpretation Pearls

                                  Selected References

                                  1. Ospel JM et al: Intra-arterial verapamil treatment in oral therapy-refractory reversible cerebral vasoconstriction syndrome. AJNR Am J Neuroradiol. 41(2):293-9, 2020
                                  2. Rocha EA et al: RCVS2 score and diagnostic approach for reversible cerebral vasoconstriction syndrome. Neurology. 92(7):e639-47, 2019
                                  3. Chen CY et al: Vascular wall imaging in reversible cerebral vasoconstriction syndrome - a 3-T contrast-enhanced MRI study. J Headache Pain. 19(1):74, 2018
                                  4. Shimoda M et al: Centripetal propagation of vasoconstriction at the time of headache resolution in patients with reversible cerebral vasoconstriction syndrome. AJNR Am J Neuroradiol. 37(9):1594-8, 2016
                                  5. Calic Z et al: The reversible cerebral vasoconstriction syndrome. Intern Med J. 45(6):599-608, 2015
                                  6. Kass-Hout T et al: A novel approach to diagnose reversible cerebral vasoconstriction syndrome: a case series. J Stroke Cerebrovasc Dis. 24(1):e31-7, 2015
                                  7. Miller TR et al: Reversible cerebral vasoconstriction syndrome, part 1: epidemiology, pathogenesis, and clinical course. AJNR Am J Neuroradiol. 36(8):1392-9, 2015
                                  8. Miller TR et al: Reversible cerebral vasoconstriction syndrome, part 2: diagnostic work-up, imaging evaluation, and differential diagnosis. AJNR Am J Neuroradiol. 36(9):1580-8, 2015
                                  9. Agarwal R et al: Posterior reversible encephalopathy and cerebral vasoconstriction in a patient with hemolytic uremic syndrome. Pediatr Neurol. 50(5):518-21, 2014
                                  10. Grooters GS et al: How often is thunderclap headache caused by the reversible cerebral vasoconstriction syndrome? Headache. 54(4):732-5, 2014
                                  11. Katz BS et al: Clinical worsening in reversible cerebral vasoconstriction syndrome. JAMA Neurol. 71(1):68-73, 2014
                                  12. Obusez EC et al: High-resolution MRI vessel wall imaging: spatial and temporal patterns of reversible cerebral vasoconstriction syndrome and central nervous system vasculitis. AJNR Am J Neuroradiol. 35(8):1527-32, 2014
                                  13. Wolff V et al: Ischaemic strokes with reversible vasoconstriction and without thunderclap headache: a variant of the reversible cerebral vasoconstriction syndrome? Cerebrovasc Dis. 39(1):31-8, 2014
                                  14. Muehlschlegel S et al: Differentiating reversible cerebral vasoconstriction syndrome with subarachnoid hemorrhage from other causes of subarachnoid hemorrhage. JAMA Neurol. 70(10):1254-60, 2013
                                  15. Marder CP et al: Multimodal imaging of reversible cerebral vasoconstriction syndrome: a series of 6 cases. AJNR Am J Neuroradiol. 33(7):1403-11, 2012
                                  16. Ducros A et al: The clinical and radiological spectrum of reversible cerebral vasoconstriction syndrome. A prospective series of 67 patients. Brain. 130(Pt 12):3091-101, 2007
                                  Related Anatomy
                                  Loading...
                                  Related Differential Diagnoses
                                  Loading...
                                  References
                                  Tables

                                  Tables

                                  KEY FACTS

                                  • Terminology

                                    • Imaging

                                      • Pathology

                                        • Clinical Issues

                                          TERMINOLOGY

                                          • Abbreviations

                                            • Reversible cerebral vasoconstriction syndrome (RCVS)

                                          • Synonyms

                                            • Call-Fleming syndrome

                                          • Definitions

                                            • Group of disorders characterized by
                                              • Reversible, multifocal cerebral artery vasoconstriction
                                              • Severe headaches (HAs) ± focal neurologic deficits

                                          IMAGING

                                          • General Features

                                            • CT Findings

                                              • MR Findings

                                                • Ultrasonographic Findings

                                                  • Angiographic Findings

                                                    DIFFERENTIAL DIAGNOSIS

                                                      PATHOLOGY

                                                      • General Features

                                                        CLINICAL ISSUES

                                                        • Presentation

                                                          • Natural History & Prognosis

                                                            • Treatment

                                                              DIAGNOSTIC CHECKLIST

                                                              • Consider

                                                                • Image Interpretation Pearls

                                                                  Selected References

                                                                  1. Ospel JM et al: Intra-arterial verapamil treatment in oral therapy-refractory reversible cerebral vasoconstriction syndrome. AJNR Am J Neuroradiol. 41(2):293-9, 2020
                                                                  2. Rocha EA et al: RCVS2 score and diagnostic approach for reversible cerebral vasoconstriction syndrome. Neurology. 92(7):e639-47, 2019
                                                                  3. Chen CY et al: Vascular wall imaging in reversible cerebral vasoconstriction syndrome - a 3-T contrast-enhanced MRI study. J Headache Pain. 19(1):74, 2018
                                                                  4. Shimoda M et al: Centripetal propagation of vasoconstriction at the time of headache resolution in patients with reversible cerebral vasoconstriction syndrome. AJNR Am J Neuroradiol. 37(9):1594-8, 2016
                                                                  5. Calic Z et al: The reversible cerebral vasoconstriction syndrome. Intern Med J. 45(6):599-608, 2015
                                                                  6. Kass-Hout T et al: A novel approach to diagnose reversible cerebral vasoconstriction syndrome: a case series. J Stroke Cerebrovasc Dis. 24(1):e31-7, 2015
                                                                  7. Miller TR et al: Reversible cerebral vasoconstriction syndrome, part 1: epidemiology, pathogenesis, and clinical course. AJNR Am J Neuroradiol. 36(8):1392-9, 2015
                                                                  8. Miller TR et al: Reversible cerebral vasoconstriction syndrome, part 2: diagnostic work-up, imaging evaluation, and differential diagnosis. AJNR Am J Neuroradiol. 36(9):1580-8, 2015
                                                                  9. Agarwal R et al: Posterior reversible encephalopathy and cerebral vasoconstriction in a patient with hemolytic uremic syndrome. Pediatr Neurol. 50(5):518-21, 2014
                                                                  10. Grooters GS et al: How often is thunderclap headache caused by the reversible cerebral vasoconstriction syndrome? Headache. 54(4):732-5, 2014
                                                                  11. Katz BS et al: Clinical worsening in reversible cerebral vasoconstriction syndrome. JAMA Neurol. 71(1):68-73, 2014
                                                                  12. Obusez EC et al: High-resolution MRI vessel wall imaging: spatial and temporal patterns of reversible cerebral vasoconstriction syndrome and central nervous system vasculitis. AJNR Am J Neuroradiol. 35(8):1527-32, 2014
                                                                  13. Wolff V et al: Ischaemic strokes with reversible vasoconstriction and without thunderclap headache: a variant of the reversible cerebral vasoconstriction syndrome? Cerebrovasc Dis. 39(1):31-8, 2014
                                                                  14. Muehlschlegel S et al: Differentiating reversible cerebral vasoconstriction syndrome with subarachnoid hemorrhage from other causes of subarachnoid hemorrhage. JAMA Neurol. 70(10):1254-60, 2013
                                                                  15. Marder CP et al: Multimodal imaging of reversible cerebral vasoconstriction syndrome: a series of 6 cases. AJNR Am J Neuroradiol. 33(7):1403-11, 2012
                                                                  16. Ducros A et al: The clinical and radiological spectrum of reversible cerebral vasoconstriction syndrome. A prospective series of 67 patients. Brain. 130(Pt 12):3091-101, 2007
                                                                  Contact UsStoreTerms and ConditionsRegistered User AgreementPrivacy PolicyHelp