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Subacute Sclerosing Panencephalitis
Kevin R. Moore, MDGary L. Hedlund, DO
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Pathology

          • Clinical Issues

            • Diagnostic Checklist

              TERMINOLOGY

              • Abbreviations

                • Subacute sclerosing panencephalitis (SSPE)
              • Synonyms

                • Dawson encephalitis
              • Definitions

                • Progressive measles virus-mediated encephalitis

              IMAGING

              • General Features

                • CT Findings

                  • MR Findings

                    • Imaging Recommendations

                      DIFFERENTIAL DIAGNOSIS

                        PATHOLOGY

                        • General Features

                          • Gross Pathologic & Surgical Features

                            • Microscopic Features

                              CLINICAL ISSUES

                              • Presentation

                                • Demographics

                                  • Natural History & Prognosis

                                    • Treatment

                                      DIAGNOSTIC CHECKLIST

                                      • Consider

                                        • Image Interpretation Pearls

                                          Selected References

                                          1. Goswami JN et al: Dystonic storm: an atypical presentation of subacute sclerosing panencephalitis. Indian Pediatr. 55(5):441, 2018
                                          2. Watanabe S et al: New insights into measles virus brain infections. Trends Microbiol. ;27(2):164-75, 2018
                                          3. Perciaccante A et al: Early and late seizures associated to Niccolò Paganini's viral encephalitis. J Neurol Sci. 382:122, 2017
                                          4. Wendorf KA et al: Subacute sclerosing panencephalitis: the devastating measles complication that might be more common than previously estimated. Clin Infect Dis. 65(2):226-32, 2017
                                          5. Fisher DL et al: Measles-induced encephalitis. QJM. 108(3):177-82, 2014
                                          6. Hatanpaa KJ et al: Neuropathology of viral infections. Handb Clin Neurol. 123:193-214, 2014
                                          7. Anlar B: Subacute sclerosing panencephalitis and chronic viral encephalitis. Handb Clin Neurol. 112:1183-9, 2013
                                          8. Buchanan R et al: Measles virus and associated central nervous system sequelae. Semin Pediatr Neurol. 19(3):107-14, 2012
                                          9. Gadoth N: Subacute sclerosing panencephalitis (SSPE) the story of a vanishing disease. Brain Dev. 34(9):705-11, 2012
                                          10. Sivadasan A et al: Fulminant subacute sclerosing panencephalitis in an individual with a perinatally acquired human immunodeficiency virus infection. Arch Neurol. 69(12):1644-7, 2012
                                          11. Cece H et al: Epidemiological findings and clinical and magnetic resonance presentations in subacute sclerosing panencephalitis. J Int Med Res. 39(2):594-602, 2011
                                          12. Handique SK: Viral infections of the central nervous system. Neuroimaging Clin N Am. 21(4):777-94, vii, 2011
                                          13. Aydin K et al: Reduced gray matter volume in the frontotemporal cortex of patients with early subacute sclerosing panencephalitis. AJNR Am J Neuroradiol. 30(2):271-5, 2009
                                          14. Oguz KK et al: MR imaging, diffusion-weighted imaging and MR spectroscopy findings in acute rapidly progressive subacute sclerosing panencephalitis. Brain Dev. 29(5):306-11, 2007
                                          15. Trivedi R et al: Assessment of white matter damage in subacute sclerosing panencephalitis using quantitative diffusion tensor MR imaging. AJNR Am J Neuroradiol. 27(8):1712-6, 2006
                                          16. Sener RN: Subacute sclerosing panencephalitis with pontine involvement. J Comput Assist Tomogr. 28(1):101-2, 2004
                                          17. Schneider-Schaulies J et al: Measles infection of the central nervous system. J Neurovirol. 9(2):247-52, 2003
                                          Related Anatomy
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                                          Related Differential Diagnoses
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                                          References
                                          Tables

                                          Tables

                                          KEY FACTS

                                          • Terminology

                                            • Imaging

                                              • Top Differential Diagnoses

                                                • Pathology

                                                  • Clinical Issues

                                                    • Diagnostic Checklist

                                                      TERMINOLOGY

                                                      • Abbreviations

                                                        • Subacute sclerosing panencephalitis (SSPE)
                                                      • Synonyms

                                                        • Dawson encephalitis
                                                      • Definitions

                                                        • Progressive measles virus-mediated encephalitis

                                                      IMAGING

                                                      • General Features

                                                        • CT Findings

                                                          • MR Findings

                                                            • Imaging Recommendations

                                                              DIFFERENTIAL DIAGNOSIS

                                                                PATHOLOGY

                                                                • General Features

                                                                  • Gross Pathologic & Surgical Features

                                                                    • Microscopic Features

                                                                      CLINICAL ISSUES

                                                                      • Presentation

                                                                        • Demographics

                                                                          • Natural History & Prognosis

                                                                            • Treatment

                                                                              DIAGNOSTIC CHECKLIST

                                                                              • Consider

                                                                                • Image Interpretation Pearls

                                                                                  Selected References

                                                                                  1. Goswami JN et al: Dystonic storm: an atypical presentation of subacute sclerosing panencephalitis. Indian Pediatr. 55(5):441, 2018
                                                                                  2. Watanabe S et al: New insights into measles virus brain infections. Trends Microbiol. ;27(2):164-75, 2018
                                                                                  3. Perciaccante A et al: Early and late seizures associated to Niccolò Paganini's viral encephalitis. J Neurol Sci. 382:122, 2017
                                                                                  4. Wendorf KA et al: Subacute sclerosing panencephalitis: the devastating measles complication that might be more common than previously estimated. Clin Infect Dis. 65(2):226-32, 2017
                                                                                  5. Fisher DL et al: Measles-induced encephalitis. QJM. 108(3):177-82, 2014
                                                                                  6. Hatanpaa KJ et al: Neuropathology of viral infections. Handb Clin Neurol. 123:193-214, 2014
                                                                                  7. Anlar B: Subacute sclerosing panencephalitis and chronic viral encephalitis. Handb Clin Neurol. 112:1183-9, 2013
                                                                                  8. Buchanan R et al: Measles virus and associated central nervous system sequelae. Semin Pediatr Neurol. 19(3):107-14, 2012
                                                                                  9. Gadoth N: Subacute sclerosing panencephalitis (SSPE) the story of a vanishing disease. Brain Dev. 34(9):705-11, 2012
                                                                                  10. Sivadasan A et al: Fulminant subacute sclerosing panencephalitis in an individual with a perinatally acquired human immunodeficiency virus infection. Arch Neurol. 69(12):1644-7, 2012
                                                                                  11. Cece H et al: Epidemiological findings and clinical and magnetic resonance presentations in subacute sclerosing panencephalitis. J Int Med Res. 39(2):594-602, 2011
                                                                                  12. Handique SK: Viral infections of the central nervous system. Neuroimaging Clin N Am. 21(4):777-94, vii, 2011
                                                                                  13. Aydin K et al: Reduced gray matter volume in the frontotemporal cortex of patients with early subacute sclerosing panencephalitis. AJNR Am J Neuroradiol. 30(2):271-5, 2009
                                                                                  14. Oguz KK et al: MR imaging, diffusion-weighted imaging and MR spectroscopy findings in acute rapidly progressive subacute sclerosing panencephalitis. Brain Dev. 29(5):306-11, 2007
                                                                                  15. Trivedi R et al: Assessment of white matter damage in subacute sclerosing panencephalitis using quantitative diffusion tensor MR imaging. AJNR Am J Neuroradiol. 27(8):1712-6, 2006
                                                                                  16. Sener RN: Subacute sclerosing panencephalitis with pontine involvement. J Comput Assist Tomogr. 28(1):101-2, 2004
                                                                                  17. Schneider-Schaulies J et al: Measles infection of the central nervous system. J Neurovirol. 9(2):247-52, 2003