Focal dilatation of umbilical vein (UV) > 9-mm diameter
Diameter 50% > intrahepatic portion of UV
UV diameter > 2 standard deviations above mean
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Novoa V et al: Perinatal outcomes of fetal intra-abdominal umbilical vein varix: a multicenter cohort study. J Matern Fetal Neonatal Med. 1-4, 2019
di Pasquo E et al: Fetal intra-abdominal umbilical vein varix: retrospective cohort study and systematic review and meta-analysis. Ultrasound Obstet Gynecol. 51(5):580-5, 2018
Lee SW et al: Clinical characteristics and outcomes of antenatal fetal intra-abdominal umbilical vein varix detection. Obstet Gynecol Sci. 57(3):181-6, 2014
Bas-Lando M et al: The prenatal diagnosis of isolated fetal varix of the intra-abdominal umbilical vein is associated with favorable neonatal outcome at term: a case series. Arch Gynecol Obstet. 288(1):33-9, 2013
Brookfield KF et al: Isolated umbilical vein varix with a poor outcome despite close fetal surveillance. J Ultrasound Med. 32(9):1680-2, 2013
Melcer Y et al: Long-term outcomes of children with umbilical vein varix diagnosed prenatally. Prenat Diagn. 33(5):492-6, 2013
Mankuta D et al: Isolated fetal intra-abdominal umbilical vein varix: clinical importance and recommendations. J Ultrasound Med. 30(2):273-6, 2011
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
TERMINOLOGY
Abbreviations
Umbilical vein varix (UVV)
Definitions
Focal dilatation of umbilical vein (UV) > 9-mm diameter
Diameter 50% > intrahepatic portion of UV
UV diameter > 2 standard deviations above mean
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
Selected References
Novoa V et al: Perinatal outcomes of fetal intra-abdominal umbilical vein varix: a multicenter cohort study. J Matern Fetal Neonatal Med. 1-4, 2019
di Pasquo E et al: Fetal intra-abdominal umbilical vein varix: retrospective cohort study and systematic review and meta-analysis. Ultrasound Obstet Gynecol. 51(5):580-5, 2018
Lee SW et al: Clinical characteristics and outcomes of antenatal fetal intra-abdominal umbilical vein varix detection. Obstet Gynecol Sci. 57(3):181-6, 2014
Bas-Lando M et al: The prenatal diagnosis of isolated fetal varix of the intra-abdominal umbilical vein is associated with favorable neonatal outcome at term: a case series. Arch Gynecol Obstet. 288(1):33-9, 2013
Brookfield KF et al: Isolated umbilical vein varix with a poor outcome despite close fetal surveillance. J Ultrasound Med. 32(9):1680-2, 2013
Melcer Y et al: Long-term outcomes of children with umbilical vein varix diagnosed prenatally. Prenat Diagn. 33(5):492-6, 2013
Mankuta D et al: Isolated fetal intra-abdominal umbilical vein varix: clinical importance and recommendations. J Ultrasound Med. 30(2):273-6, 2011
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