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Umbilical Vein Varix
Anne Kennedy, MD
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KEY FACTS

  • Terminology

    • Imaging

      • Top Differential Diagnoses

        • Clinical Issues

          TERMINOLOGY

          • Abbreviations

            • Umbilical vein varix (UVV)
          • Definitions

            • Focal dilatation of umbilical vein (UV) > 9-mm diameter
            • Diameter 50% > intrahepatic portion of UV
            • UV diameter > 2 standard deviations above mean

          IMAGING

          • General Features

            • Ultrasonographic Findings

              • Imaging Recommendations

                DIFFERENTIAL DIAGNOSIS

                  PATHOLOGY

                  • General Features

                    • Gross Pathologic & Surgical Features

                      CLINICAL ISSUES

                      • Presentation

                        • Demographics

                          • Natural History & Prognosis

                            • Treatment

                              Selected References

                              1. Novoa V et al: Perinatal outcomes of fetal intra-abdominal umbilical vein varix: a multicenter cohort study. J Matern Fetal Neonatal Med. 1-4, 2019
                              2. di Pasquo E et al: Fetal intra-abdominal umbilical vein varix: retrospective cohort study and systematic review and meta-analysis. Ultrasound Obstet Gynecol. 51(5):580-5, 2018
                              3. Lee SW et al: Clinical characteristics and outcomes of antenatal fetal intra-abdominal umbilical vein varix detection. Obstet Gynecol Sci. 57(3):181-6, 2014
                              4. Bas-Lando M et al: The prenatal diagnosis of isolated fetal varix of the intra-abdominal umbilical vein is associated with favorable neonatal outcome at term: a case series. Arch Gynecol Obstet. 288(1):33-9, 2013
                              5. Brookfield KF et al: Isolated umbilical vein varix with a poor outcome despite close fetal surveillance. J Ultrasound Med. 32(9):1680-2, 2013
                              6. Melcer Y et al: Long-term outcomes of children with umbilical vein varix diagnosed prenatally. Prenat Diagn. 33(5):492-6, 2013
                              7. Mankuta D et al: Isolated fetal intra-abdominal umbilical vein varix: clinical importance and recommendations. J Ultrasound Med. 30(2):273-6, 2011
                              Related Anatomy
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                              Related Differential Diagnoses
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                              References
                              Tables

                              Tables

                              KEY FACTS

                              • Terminology

                                • Imaging

                                  • Top Differential Diagnoses

                                    • Clinical Issues

                                      TERMINOLOGY

                                      • Abbreviations

                                        • Umbilical vein varix (UVV)
                                      • Definitions

                                        • Focal dilatation of umbilical vein (UV) > 9-mm diameter
                                        • Diameter 50% > intrahepatic portion of UV
                                        • UV diameter > 2 standard deviations above mean

                                      IMAGING

                                      • General Features

                                        • Ultrasonographic Findings

                                          • Imaging Recommendations

                                            DIFFERENTIAL DIAGNOSIS

                                              PATHOLOGY

                                              • General Features

                                                • Gross Pathologic & Surgical Features

                                                  CLINICAL ISSUES

                                                  • Presentation

                                                    • Demographics

                                                      • Natural History & Prognosis

                                                        • Treatment

                                                          Selected References

                                                          1. Novoa V et al: Perinatal outcomes of fetal intra-abdominal umbilical vein varix: a multicenter cohort study. J Matern Fetal Neonatal Med. 1-4, 2019
                                                          2. di Pasquo E et al: Fetal intra-abdominal umbilical vein varix: retrospective cohort study and systematic review and meta-analysis. Ultrasound Obstet Gynecol. 51(5):580-5, 2018
                                                          3. Lee SW et al: Clinical characteristics and outcomes of antenatal fetal intra-abdominal umbilical vein varix detection. Obstet Gynecol Sci. 57(3):181-6, 2014
                                                          4. Bas-Lando M et al: The prenatal diagnosis of isolated fetal varix of the intra-abdominal umbilical vein is associated with favorable neonatal outcome at term: a case series. Arch Gynecol Obstet. 288(1):33-9, 2013
                                                          5. Brookfield KF et al: Isolated umbilical vein varix with a poor outcome despite close fetal surveillance. J Ultrasound Med. 32(9):1680-2, 2013
                                                          6. Melcer Y et al: Long-term outcomes of children with umbilical vein varix diagnosed prenatally. Prenat Diagn. 33(5):492-6, 2013
                                                          7. Mankuta D et al: Isolated fetal intra-abdominal umbilical vein varix: clinical importance and recommendations. J Ultrasound Med. 30(2):273-6, 2011