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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
TERMINOLOGY
Abbreviations
Umbilical vein varix (UVV)
Definitions
Focal dilatation of umbilical vein (UV) > 9-mm diameter
Diameter 50% > intrahepatic portion of UV
UV diameter > 2 standard deviations above mean
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Lee SW et al: Clinical characteristics and outcomes of antenatal fetal intra-abdominal umbilical vein varix detection. Obstet Gynecol Sci. 57(3):181-6, 2014
Bas-Lando M et al: The prenatal diagnosis of isolated fetal varix of the intra-abdominal umbilical vein is associated with favorable neonatal outcome at term: a case series. Arch Gynecol Obstet. 288(1):33-9, 2013
Brookfield KF et al: Isolated umbilical vein varix with a poor outcome despite close fetal surveillance. J Ultrasound Med. 32(9):1680-2, 2013
Kanenishi K et al: HDlive imaging of intra-amniotic umbilical vein varix with thrombosis. Placenta. 34(11):1110-2, 2013
Melcer Y et al: Long-term outcomes of children with umbilical vein varix diagnosed prenatally. Prenat Diagn. 33(5):492-6, 2013
Sanapo L et al: Four cases of fetal intra-abdominal umbilical vein varix: a single centre's approach to management. J Obstet Gynaecol. 33(4):375-7, 2013
Cohen Y et al: Ultrasonographic evidence of intra-abdominal umbilical vein dilatation: is it a true varix? Ultrasound Med Biol. 38(3):412-6, 2012
Lu M et al: Two- and three-dimensional sonographic diagnosis of fetal intra-abdominal umbilical vein varix: a case report. J Clin Ultrasound. 40(9):586-9, 2012
Mankuta D et al: Isolated fetal intra-abdominal umbilical vein varix: clinical importance and recommendations. J Ultrasound Med. 30(2):273-6, 2011
Vanrykel K et al: Neonatal disseminated intravascular coagulation after thrombosis of a fetal intra-abdominal umbilical vein varix. J Obstet Gynaecol. 30(3):315, 2010
Byers BD et al: Pregnancy outcome after ultrasound diagnosis of fetal intra-abdominal umbilical vein varix. Ultrasound Obstet Gynecol. 33(3):282-6, 2009
Fung TY et al: Gastroschisis associated with an intra-abdominal umbilical vein varix: a report of 2 cases. Fetal Diagn Ther. 25(4):404-6, 2009
Weissmann-Brenner A et al: Isolated fetal umbilical vein varix--prenatal sonographic diagnosis and suggested management. Prenat Diagn. 29(3):229-33, 2009
Ranka P et al: Fetal intra-abdominal umbilical vein varix. J Obstet Gynaecol. 28(7):747-8, 2008
Fung TY et al: Fetal intra-abdominal umbilical vein varix: what is the clinical significance? Ultrasound Obstet Gynecol. 25(2):149-54, 2005
Valsky DV et al: Adverse outcome of isolated fetal intra-abdominal umbilical vein varix despite close monitoring. Prenat Diagn. 24(6):451-4, 2004
Viora E et al: Anomalies of the fetal venous system: a report of 26 cases and review of the literature. Fetal Diagn Ther. 19(5):440-7, 2004
Zachariah M et al: Umbilical vein varix thrombosis: a rare pathology. J Obstet Gynaecol. 24(5):581, 2004
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Clinical Issues
TERMINOLOGY
Abbreviations
Umbilical vein varix (UVV)
Definitions
Focal dilatation of umbilical vein (UV) > 9-mm diameter
Diameter 50% > intrahepatic portion of UV
UV diameter > 2 standard deviations above mean
IMAGING
General Features
Ultrasonographic Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Selected References
Lee SW et al: Clinical characteristics and outcomes of antenatal fetal intra-abdominal umbilical vein varix detection. Obstet Gynecol Sci. 57(3):181-6, 2014
Bas-Lando M et al: The prenatal diagnosis of isolated fetal varix of the intra-abdominal umbilical vein is associated with favorable neonatal outcome at term: a case series. Arch Gynecol Obstet. 288(1):33-9, 2013
Brookfield KF et al: Isolated umbilical vein varix with a poor outcome despite close fetal surveillance. J Ultrasound Med. 32(9):1680-2, 2013
Kanenishi K et al: HDlive imaging of intra-amniotic umbilical vein varix with thrombosis. Placenta. 34(11):1110-2, 2013
Melcer Y et al: Long-term outcomes of children with umbilical vein varix diagnosed prenatally. Prenat Diagn. 33(5):492-6, 2013
Sanapo L et al: Four cases of fetal intra-abdominal umbilical vein varix: a single centre's approach to management. J Obstet Gynaecol. 33(4):375-7, 2013
Cohen Y et al: Ultrasonographic evidence of intra-abdominal umbilical vein dilatation: is it a true varix? Ultrasound Med Biol. 38(3):412-6, 2012
Lu M et al: Two- and three-dimensional sonographic diagnosis of fetal intra-abdominal umbilical vein varix: a case report. J Clin Ultrasound. 40(9):586-9, 2012
Mankuta D et al: Isolated fetal intra-abdominal umbilical vein varix: clinical importance and recommendations. J Ultrasound Med. 30(2):273-6, 2011
Vanrykel K et al: Neonatal disseminated intravascular coagulation after thrombosis of a fetal intra-abdominal umbilical vein varix. J Obstet Gynaecol. 30(3):315, 2010
Byers BD et al: Pregnancy outcome after ultrasound diagnosis of fetal intra-abdominal umbilical vein varix. Ultrasound Obstet Gynecol. 33(3):282-6, 2009
Fung TY et al: Gastroschisis associated with an intra-abdominal umbilical vein varix: a report of 2 cases. Fetal Diagn Ther. 25(4):404-6, 2009
Weissmann-Brenner A et al: Isolated fetal umbilical vein varix--prenatal sonographic diagnosis and suggested management. Prenat Diagn. 29(3):229-33, 2009
Ranka P et al: Fetal intra-abdominal umbilical vein varix. J Obstet Gynaecol. 28(7):747-8, 2008
Fung TY et al: Fetal intra-abdominal umbilical vein varix: what is the clinical significance? Ultrasound Obstet Gynecol. 25(2):149-54, 2005
Valsky DV et al: Adverse outcome of isolated fetal intra-abdominal umbilical vein varix despite close monitoring. Prenat Diagn. 24(6):451-4, 2004
Viora E et al: Anomalies of the fetal venous system: a report of 26 cases and review of the literature. Fetal Diagn Ther. 19(5):440-7, 2004
Zachariah M et al: Umbilical vein varix thrombosis: a rare pathology. J Obstet Gynaecol. 24(5):581, 2004
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