link
Bookmarks
Obstetrics
Diagnosis
Genitourinary Tract
Renal Developmental Variants
Unilateral Renal Agenesis
Unilateral Renal Agenesis
Priyanka Jha, MBBS
To access 4,300 diagnoses written by the world's leading experts in radiology.Try it free - 15 days
0
3
0
0

KEY FACTS

  • Imaging

    • Top Differential Diagnoses

      • Pathology

        • Clinical Issues

          • Diagnostic Checklist

            TERMINOLOGY

            • Abbreviations

              • Renal agenesis (RA)

            • Definitions

              • Absent unilateral kidney
                • Failure of development

            IMAGING

            • General Features

              • Ultrasonographic Findings

                • MR Findings

                  • Imaging Recommendations

                    DIFFERENTIAL DIAGNOSIS

                      PATHOLOGY

                      • General Features

                        CLINICAL ISSUES

                        • Presentation

                          • Demographics

                            • Natural History & Prognosis

                              • Treatment

                                DIAGNOSTIC CHECKLIST

                                • Image Interpretation Pearls

                                  Selected References

                                  1. Güngör T et al: Retrospective evaluation of children with unilateral renal agenesis. Pediatr Nephrol. ePub, 2021
                                  2. Gungor Ugurlucan F et al: Diagnosis, management, and outcome of obstructed hemivagina and ipsilateral renal agenesis (OHVIRA syndrome): is there a correlation between MRI findings and outcome? Clin Imaging. 59(2):172-8, 2020
                                  3. Friedman MA et al: Screening for mullerian anomalies in patients with unilateral renal agenesis: Leveraging early detection to prevent complications. J Pediatr Urol. 14(2):144-9, 2018
                                  4. Laurichesse Delmas H et al: Congenital unilateral renal agenesis: prevalence, prenatal diagnosis, associated anomalies. Data from two birth-defect registries. Birth Defects Res. 109(15):1204-11, 2017
                                  5. Rosenblum S et al: Renal development in the fetus and premature infant. Semin Fetal Neonatal Med. 22(2):58-66, 2017
                                  6. Clinton CM et al: Unilateral fetal renal abnormalities: are they really isolated? J Ultrasound Med. 35(3):561-4, 2016
                                  7. Duval H et al: Fetal anomalies associated with HNF1B mutations: report of 20 autopsy cases. Prenat Diagn. 36(8):744-51, 2016
                                  8. Perlman S et al: Prenatal compensatory renal growth in unilateral renal agenesis. Prenat Diagn. 36(11):1075-80, 2016
                                  9. Shah K et al: Spectrum of urorectal septum malformation sequence. Congenit Anom (Kyoto). 56(3):119-26, 2016
                                  10. Acién P et al: Reproductive outcome in uterine malformations with or without an associated unilateral renal agenesis. J Reprod Med. 59(1-2):69-75, 2014
                                  11. Cunningham BK et al: Analysis of renal anomalies in VACTERL association. Birth Defects Res A Clin Mol Teratol. 100(10):801-5, 2014
                                  12. Doğan ÇS et al: Renal outcome of children with unilateral renal agenesis. Turk J Pediatr. 55(6):612-5, 2013
                                  13. Wang S et al: Duplicated uterus and hemivaginal or hemicervical atresia with ipsilateral renal agenesis: an institutional clinical series of 52 cases. Eur J Obstet Gynecol Reprod Biol. 170(2):507-11, 2013
                                  14. Westland R et al: Unilateral renal agenesis: a systematic review on associated anomalies and renal injury. Nephrol Dial Transplant. 28(7):1844-55, 2013
                                  15. van Vuuren SH et al: Compensatory enlargement of a solitary functioning kidney during fetal development. Ultrasound Obstet Gynecol. 40(6):665-8, 2012
                                  16. Cho JY et al: Measurement of compensatory hyperplasia of the contralateral kidney: usefulness for differential diagnosis of fetal unilateral empty renal fossa. Ultrasound Obstet Gynecol. 34(5):515-20, 2009
                                  17. Jindal G et al: Uterus didelphys with unilateral obstructed hemivagina with hematometrocolpos and hematosalpinx with ipsilateral renal agenesis. J Hum Reprod Sci. 2(2):87-9, 2009
                                  18. Sanna-Cherchi S et al: Renal outcome in patients with congenital anomalies of the kidney and urinary tract. Kidney Int. 76(5):528-33, 2009
                                  19. Hiraoka M et al: Renal aplasia is the predominant cause of congenital solitary kidneys. Kidney Int. 61(5):1840-4, 2002
                                  20. Huang HM et al: Auditory abnormalities associated with unilateral renal agenesis. Int J Pediatr Otorhinolaryngol. 60(2):113-8, 2001
                                  Related Anatomy
                                  Loading...
                                  Related Differential Diagnoses
                                  Loading...
                                  References
                                  Tables

                                  Tables

                                  KEY FACTS

                                  • Imaging

                                    • Top Differential Diagnoses

                                      • Pathology

                                        • Clinical Issues

                                          • Diagnostic Checklist

                                            TERMINOLOGY

                                            • Abbreviations

                                              • Renal agenesis (RA)

                                            • Definitions

                                              • Absent unilateral kidney
                                                • Failure of development

                                            IMAGING

                                            • General Features

                                              • Ultrasonographic Findings

                                                • MR Findings

                                                  • Imaging Recommendations

                                                    DIFFERENTIAL DIAGNOSIS

                                                      PATHOLOGY

                                                      • General Features

                                                        CLINICAL ISSUES

                                                        • Presentation

                                                          • Demographics

                                                            • Natural History & Prognosis

                                                              • Treatment

                                                                DIAGNOSTIC CHECKLIST

                                                                • Image Interpretation Pearls

                                                                  Selected References

                                                                  1. Güngör T et al: Retrospective evaluation of children with unilateral renal agenesis. Pediatr Nephrol. ePub, 2021
                                                                  2. Gungor Ugurlucan F et al: Diagnosis, management, and outcome of obstructed hemivagina and ipsilateral renal agenesis (OHVIRA syndrome): is there a correlation between MRI findings and outcome? Clin Imaging. 59(2):172-8, 2020
                                                                  3. Friedman MA et al: Screening for mullerian anomalies in patients with unilateral renal agenesis: Leveraging early detection to prevent complications. J Pediatr Urol. 14(2):144-9, 2018
                                                                  4. Laurichesse Delmas H et al: Congenital unilateral renal agenesis: prevalence, prenatal diagnosis, associated anomalies. Data from two birth-defect registries. Birth Defects Res. 109(15):1204-11, 2017
                                                                  5. Rosenblum S et al: Renal development in the fetus and premature infant. Semin Fetal Neonatal Med. 22(2):58-66, 2017
                                                                  6. Clinton CM et al: Unilateral fetal renal abnormalities: are they really isolated? J Ultrasound Med. 35(3):561-4, 2016
                                                                  7. Duval H et al: Fetal anomalies associated with HNF1B mutations: report of 20 autopsy cases. Prenat Diagn. 36(8):744-51, 2016
                                                                  8. Perlman S et al: Prenatal compensatory renal growth in unilateral renal agenesis. Prenat Diagn. 36(11):1075-80, 2016
                                                                  9. Shah K et al: Spectrum of urorectal septum malformation sequence. Congenit Anom (Kyoto). 56(3):119-26, 2016
                                                                  10. Acién P et al: Reproductive outcome in uterine malformations with or without an associated unilateral renal agenesis. J Reprod Med. 59(1-2):69-75, 2014
                                                                  11. Cunningham BK et al: Analysis of renal anomalies in VACTERL association. Birth Defects Res A Clin Mol Teratol. 100(10):801-5, 2014
                                                                  12. Doğan ÇS et al: Renal outcome of children with unilateral renal agenesis. Turk J Pediatr. 55(6):612-5, 2013
                                                                  13. Wang S et al: Duplicated uterus and hemivaginal or hemicervical atresia with ipsilateral renal agenesis: an institutional clinical series of 52 cases. Eur J Obstet Gynecol Reprod Biol. 170(2):507-11, 2013
                                                                  14. Westland R et al: Unilateral renal agenesis: a systematic review on associated anomalies and renal injury. Nephrol Dial Transplant. 28(7):1844-55, 2013
                                                                  15. van Vuuren SH et al: Compensatory enlargement of a solitary functioning kidney during fetal development. Ultrasound Obstet Gynecol. 40(6):665-8, 2012
                                                                  16. Cho JY et al: Measurement of compensatory hyperplasia of the contralateral kidney: usefulness for differential diagnosis of fetal unilateral empty renal fossa. Ultrasound Obstet Gynecol. 34(5):515-20, 2009
                                                                  17. Jindal G et al: Uterus didelphys with unilateral obstructed hemivagina with hematometrocolpos and hematosalpinx with ipsilateral renal agenesis. J Hum Reprod Sci. 2(2):87-9, 2009
                                                                  18. Sanna-Cherchi S et al: Renal outcome in patients with congenital anomalies of the kidney and urinary tract. Kidney Int. 76(5):528-33, 2009
                                                                  19. Hiraoka M et al: Renal aplasia is the predominant cause of congenital solitary kidneys. Kidney Int. 61(5):1840-4, 2002
                                                                  20. Huang HM et al: Auditory abnormalities associated with unilateral renal agenesis. Int J Pediatr Otorhinolaryngol. 60(2):113-8, 2001