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Unilateral Renal Agenesis
Priyanka Jha, MBBS
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KEY FACTS

  • Imaging

    • Top Differential Diagnoses

      • Pathology

        • Clinical Issues

          • Diagnostic Checklist

            TERMINOLOGY

            • Abbreviations

              • Renal agenesis (RA)
            • Definitions

              • Absent unilateral kidney
                • Failure of development

            IMAGING

            • General Features

              • Ultrasonographic Findings

                • MR Findings

                  • Imaging Recommendations

                    DIFFERENTIAL DIAGNOSIS

                      PATHOLOGY

                      • General Features

                        CLINICAL ISSUES

                        • Presentation

                          • Demographics

                            • Natural History & Prognosis

                              • Treatment

                                DIAGNOSTIC CHECKLIST

                                • Image Interpretation Pearls

                                  Selected References

                                  1. Güngör T et al: Retrospective evaluation of children with unilateral renal agenesis. Pediatr Nephrol. ePub, 2021
                                  2. Gungor Ugurlucan F et al: Diagnosis, management, and outcome of obstructed hemivagina and ipsilateral renal agenesis (OHVIRA syndrome): is there a correlation between MRI findings and outcome? Clin Imaging. 59(2):172-8, 2020
                                  3. Friedman MA et al: Screening for mullerian anomalies in patients with unilateral renal agenesis: Leveraging early detection to prevent complications. J Pediatr Urol. 14(2):144-9, 2018
                                  4. Laurichesse Delmas H et al: Congenital unilateral renal agenesis: prevalence, prenatal diagnosis, associated anomalies. Data from two birth-defect registries. Birth Defects Res. 109(15):1204-11, 2017
                                  5. Rosenblum S et al: Renal development in the fetus and premature infant. Semin Fetal Neonatal Med. 22(2):58-66, 2017
                                  6. Clinton CM et al: Unilateral fetal renal abnormalities: are they really isolated? J Ultrasound Med. 35(3):561-4, 2016
                                  7. Duval H et al: Fetal anomalies associated with HNF1B mutations: report of 20 autopsy cases. Prenat Diagn. 36(8):744-51, 2016
                                  8. Perlman S et al: Prenatal compensatory renal growth in unilateral renal agenesis. Prenat Diagn. 36(11):1075-80, 2016
                                  9. Shah K et al: Spectrum of urorectal septum malformation sequence. Congenit Anom (Kyoto). 56(3):119-26, 2016
                                  10. Acién P et al: Reproductive outcome in uterine malformations with or without an associated unilateral renal agenesis. J Reprod Med. 59(1-2):69-75, 2014
                                  11. Cunningham BK et al: Analysis of renal anomalies in VACTERL association. Birth Defects Res A Clin Mol Teratol. 100(10):801-5, 2014
                                  12. Doğan ÇS et al: Renal outcome of children with unilateral renal agenesis. Turk J Pediatr. 55(6):612-5, 2013
                                  13. Wang S et al: Duplicated uterus and hemivaginal or hemicervical atresia with ipsilateral renal agenesis: an institutional clinical series of 52 cases. Eur J Obstet Gynecol Reprod Biol. 170(2):507-11, 2013
                                  14. Westland R et al: Unilateral renal agenesis: a systematic review on associated anomalies and renal injury. Nephrol Dial Transplant. 28(7):1844-55, 2013
                                  15. van Vuuren SH et al: Compensatory enlargement of a solitary functioning kidney during fetal development. Ultrasound Obstet Gynecol. 40(6):665-8, 2012
                                  16. Cho JY et al: Measurement of compensatory hyperplasia of the contralateral kidney: usefulness for differential diagnosis of fetal unilateral empty renal fossa. Ultrasound Obstet Gynecol. 34(5):515-20, 2009
                                  17. Jindal G et al: Uterus didelphys with unilateral obstructed hemivagina with hematometrocolpos and hematosalpinx with ipsilateral renal agenesis. J Hum Reprod Sci. 2(2):87-9, 2009
                                  18. Sanna-Cherchi S et al: Renal outcome in patients with congenital anomalies of the kidney and urinary tract. Kidney Int. 76(5):528-33, 2009
                                  19. Hiraoka M et al: Renal aplasia is the predominant cause of congenital solitary kidneys. Kidney Int. 61(5):1840-4, 2002
                                  20. Huang HM et al: Auditory abnormalities associated with unilateral renal agenesis. Int J Pediatr Otorhinolaryngol. 60(2):113-8, 2001
                                  Related Anatomy
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                                  Related Differential Diagnoses
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                                  References
                                  Tables

                                  Tables

                                  KEY FACTS

                                  • Imaging

                                    • Top Differential Diagnoses

                                      • Pathology

                                        • Clinical Issues

                                          • Diagnostic Checklist

                                            TERMINOLOGY

                                            • Abbreviations

                                              • Renal agenesis (RA)
                                            • Definitions

                                              • Absent unilateral kidney
                                                • Failure of development

                                            IMAGING

                                            • General Features

                                              • Ultrasonographic Findings

                                                • MR Findings

                                                  • Imaging Recommendations

                                                    DIFFERENTIAL DIAGNOSIS

                                                      PATHOLOGY

                                                      • General Features

                                                        CLINICAL ISSUES

                                                        • Presentation

                                                          • Demographics

                                                            • Natural History & Prognosis

                                                              • Treatment

                                                                DIAGNOSTIC CHECKLIST

                                                                • Image Interpretation Pearls

                                                                  Selected References

                                                                  1. Güngör T et al: Retrospective evaluation of children with unilateral renal agenesis. Pediatr Nephrol. ePub, 2021
                                                                  2. Gungor Ugurlucan F et al: Diagnosis, management, and outcome of obstructed hemivagina and ipsilateral renal agenesis (OHVIRA syndrome): is there a correlation between MRI findings and outcome? Clin Imaging. 59(2):172-8, 2020
                                                                  3. Friedman MA et al: Screening for mullerian anomalies in patients with unilateral renal agenesis: Leveraging early detection to prevent complications. J Pediatr Urol. 14(2):144-9, 2018
                                                                  4. Laurichesse Delmas H et al: Congenital unilateral renal agenesis: prevalence, prenatal diagnosis, associated anomalies. Data from two birth-defect registries. Birth Defects Res. 109(15):1204-11, 2017
                                                                  5. Rosenblum S et al: Renal development in the fetus and premature infant. Semin Fetal Neonatal Med. 22(2):58-66, 2017
                                                                  6. Clinton CM et al: Unilateral fetal renal abnormalities: are they really isolated? J Ultrasound Med. 35(3):561-4, 2016
                                                                  7. Duval H et al: Fetal anomalies associated with HNF1B mutations: report of 20 autopsy cases. Prenat Diagn. 36(8):744-51, 2016
                                                                  8. Perlman S et al: Prenatal compensatory renal growth in unilateral renal agenesis. Prenat Diagn. 36(11):1075-80, 2016
                                                                  9. Shah K et al: Spectrum of urorectal septum malformation sequence. Congenit Anom (Kyoto). 56(3):119-26, 2016
                                                                  10. Acién P et al: Reproductive outcome in uterine malformations with or without an associated unilateral renal agenesis. J Reprod Med. 59(1-2):69-75, 2014
                                                                  11. Cunningham BK et al: Analysis of renal anomalies in VACTERL association. Birth Defects Res A Clin Mol Teratol. 100(10):801-5, 2014
                                                                  12. Doğan ÇS et al: Renal outcome of children with unilateral renal agenesis. Turk J Pediatr. 55(6):612-5, 2013
                                                                  13. Wang S et al: Duplicated uterus and hemivaginal or hemicervical atresia with ipsilateral renal agenesis: an institutional clinical series of 52 cases. Eur J Obstet Gynecol Reprod Biol. 170(2):507-11, 2013
                                                                  14. Westland R et al: Unilateral renal agenesis: a systematic review on associated anomalies and renal injury. Nephrol Dial Transplant. 28(7):1844-55, 2013
                                                                  15. van Vuuren SH et al: Compensatory enlargement of a solitary functioning kidney during fetal development. Ultrasound Obstet Gynecol. 40(6):665-8, 2012
                                                                  16. Cho JY et al: Measurement of compensatory hyperplasia of the contralateral kidney: usefulness for differential diagnosis of fetal unilateral empty renal fossa. Ultrasound Obstet Gynecol. 34(5):515-20, 2009
                                                                  17. Jindal G et al: Uterus didelphys with unilateral obstructed hemivagina with hematometrocolpos and hematosalpinx with ipsilateral renal agenesis. J Hum Reprod Sci. 2(2):87-9, 2009
                                                                  18. Sanna-Cherchi S et al: Renal outcome in patients with congenital anomalies of the kidney and urinary tract. Kidney Int. 76(5):528-33, 2009
                                                                  19. Hiraoka M et al: Renal aplasia is the predominant cause of congenital solitary kidneys. Kidney Int. 61(5):1840-4, 2002
                                                                  20. Huang HM et al: Auditory abnormalities associated with unilateral renal agenesis. Int J Pediatr Otorhinolaryngol. 60(2):113-8, 2001