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Chest
Diagnosis
Airway Diseases
Airway Narrowing and Wall Thickening
Wegener Granulomatosis, Airway
Wegener Granulomatosis, Airway
Jeffrey P. Kanne, MD
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Wegener granulomatosis (WG)
Synonyms
Granulomatous polyangiitis,
granulomatosis with polyangiitis
(newly accepted name for WG)
Definitions
Multisystemic necrotizing granulomatous vasculitis of small to medium vessels without associated infection
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Kallenberg CG: Pathogenesis of ANCA-associated vasculitides. Ann Rheum Dis. 70 Suppl 1:i59-63, 2011
Langford CA: Cyclophosphamide as induction therapy for Wegener's granulomatosis and microscopic polyangiitis. Clin Exp Immunol. 164 Suppl 1:31-4, 2011
Niles J: Rituximab in induction therapy for anti-neutrophil cytoplasmic antibody (ANCA) vasculitis. Clin Exp Immunol. 164 Suppl 1:27-30, 2011
Schilder AM: Wegener's Granulomatosis vasculitis and granuloma. Autoimmun Rev. 9(7):483-7, 2010
Ananthakrishnan L et al: Wegener's granulomatosis in the chest: high-resolution CT findings. AJR Am J Roentgenol. 192(3):676-82, 2009
Carruthers D et al: Evidence-based management of ANCA vasculitis. Best Pract Res Clin Rheumatol. 23(3):367-78, 2009
Grenier PA et al: Nonneoplastic tracheal and bronchial stenoses. Radiol Clin North Am. 47(2):243-60, 2009
Turnbull J et al: Adverse effects of therapy for ANCA-associated vasculitis. Best Pract Res Clin Rheumatol. 23(3):391-401, 2009
Jagiello P et al: Complex genetics of Wegener granulomatosis. Autoimmun Rev. 4(1):42-7, 2005
Daum TE et al: Tracheobronchial involvement in Wegener's granulomatosis. Am J Respir Crit Care Med. 151(2 Pt 1):522-6, 1995
Hoffman GS et al: Wegener granulomatosis: an analysis of 158 patients. Ann Intern Med. 116(6):488-98, 1992
Aberle DR et al: Thoracic manifestations of Wegener granulomatosis: diagnosis and course. Radiology. 174(3 Pt 1):703-9, 1990
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
Diagnostic Checklist
TERMINOLOGY
Abbreviations
Wegener granulomatosis (WG)
Synonyms
Granulomatous polyangiitis,
granulomatosis with polyangiitis
(newly accepted name for WG)
Definitions
Multisystemic necrotizing granulomatous vasculitis of small to medium vessels without associated infection
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Staging, Grading, & Classification
Gross Pathologic & Surgical Features
Microscopic Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Kallenberg CG: Pathogenesis of ANCA-associated vasculitides. Ann Rheum Dis. 70 Suppl 1:i59-63, 2011
Langford CA: Cyclophosphamide as induction therapy for Wegener's granulomatosis and microscopic polyangiitis. Clin Exp Immunol. 164 Suppl 1:31-4, 2011
Niles J: Rituximab in induction therapy for anti-neutrophil cytoplasmic antibody (ANCA) vasculitis. Clin Exp Immunol. 164 Suppl 1:27-30, 2011
Schilder AM: Wegener's Granulomatosis vasculitis and granuloma. Autoimmun Rev. 9(7):483-7, 2010
Ananthakrishnan L et al: Wegener's granulomatosis in the chest: high-resolution CT findings. AJR Am J Roentgenol. 192(3):676-82, 2009
Carruthers D et al: Evidence-based management of ANCA vasculitis. Best Pract Res Clin Rheumatol. 23(3):367-78, 2009
Grenier PA et al: Nonneoplastic tracheal and bronchial stenoses. Radiol Clin North Am. 47(2):243-60, 2009
Turnbull J et al: Adverse effects of therapy for ANCA-associated vasculitis. Best Pract Res Clin Rheumatol. 23(3):391-401, 2009
Jagiello P et al: Complex genetics of Wegener granulomatosis. Autoimmun Rev. 4(1):42-7, 2005
Daum TE et al: Tracheobronchial involvement in Wegener's granulomatosis. Am J Respir Crit Care Med. 151(2 Pt 1):522-6, 1995
Hoffman GS et al: Wegener granulomatosis: an analysis of 158 patients. Ann Intern Med. 116(6):488-98, 1992
Aberle DR et al: Thoracic manifestations of Wegener granulomatosis: diagnosis and course. Radiology. 174(3 Pt 1):703-9, 1990
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