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Williams-Campbell Syndrome
Williams-Campbell Syndrome
Sonia L. Betancourt-Cuellar, MD
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KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Williams-Campbell syndrome (WCS)
Synonyms
Bronchomalacia
Noncystic fibrosis
Definitions
Rare congenital syndrome characterized by partial or complete absence of cartilage in subsegmental bronchi
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Singh A et al: Bronchiectasis revisited: imaging-based pattern approach to diagnosis. Curr Probl Diagn Radiol. 48(1):53-60, 2019
Marini T et al: Beyond bronchitis: a review of the congenital and acquired abnormalities of the bronchus. Insights Imaging. 8(1):141-53, 2017
Milliron B et al: Bronchiectasis: mechanisms and imaging clues of associated common and uncommon diseases. Radiographics. 35(4):1011-30, 2015
Noriega Aldave AP et al: The clinical manifestations, diagnosis and management of williams-campbell syndrome. N Am J Med Sci. 6(9):429-32, 2014
Related Anatomy
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Related Differential Diagnoses
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References
Tables
Tables
KEY FACTS
Terminology
Imaging
Top Differential Diagnoses
Pathology
Clinical Issues
TERMINOLOGY
Abbreviations
Williams-Campbell syndrome (WCS)
Synonyms
Bronchomalacia
Noncystic fibrosis
Definitions
Rare congenital syndrome characterized by partial or complete absence of cartilage in subsegmental bronchi
IMAGING
General Features
Radiographic Findings
CT Findings
Imaging Recommendations
DIFFERENTIAL DIAGNOSIS
PATHOLOGY
General Features
Gross Pathologic & Surgical Features
CLINICAL ISSUES
Presentation
Demographics
Natural History & Prognosis
Treatment
DIAGNOSTIC CHECKLIST
Consider
Image Interpretation Pearls
Selected References
Singh A et al: Bronchiectasis revisited: imaging-based pattern approach to diagnosis. Curr Probl Diagn Radiol. 48(1):53-60, 2019
Marini T et al: Beyond bronchitis: a review of the congenital and acquired abnormalities of the bronchus. Insights Imaging. 8(1):141-53, 2017
Milliron B et al: Bronchiectasis: mechanisms and imaging clues of associated common and uncommon diseases. Radiographics. 35(4):1011-30, 2015
Noriega Aldave AP et al: The clinical manifestations, diagnosis and management of williams-campbell syndrome. N Am J Med Sci. 6(9):429-32, 2014
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